Is survival in Myotonic Dystrophy improved by chronic ventilatory support?

C. Seijger (Groningen, Netherlands), J. Raaphorst (Amsterdam, Netherlands), J. Vonk (Groningen, Netherlands), B. Engelen, Van (Nijmegen, Netherlands), N. Stigter (Utrecht, Netherlands), P. Wijkstra (Groningen, Netherlands)

Source: International Congress 2019 – Treatment of chronic respiratory failure with noninvasive ventilation
Session: Treatment of chronic respiratory failure with noninvasive ventilation
Session type: Thematic Poster
Number: 2300
Disease area: Respiratory critical care, Sleep and breathing disorders

Congress or journal article abstractE-poster

Rating: 0
You must login to grade this presentation.

Share or cite this content

Citations should be made in the following way:
C. Seijger (Groningen, Netherlands), J. Raaphorst (Amsterdam, Netherlands), J. Vonk (Groningen, Netherlands), B. Engelen, Van (Nijmegen, Netherlands), N. Stigter (Utrecht, Netherlands), P. Wijkstra (Groningen, Netherlands). Is survival in Myotonic Dystrophy improved by chronic ventilatory support?. 2300

You must login to share this Presentation/Article on Twitter, Facebook, LinkedIn or by email.

Member's Comments

No comment yet.
You must Login to comment this presentation.


Related content which might interest you:
Evolution and survival of patients with Myotonic Distrophy and non-invasive ventilation.
Source: International Congress 2017 – Noninvasive ventilation for chronic respiratory failure
Year: 2017


Effect on survival of long-term non-invasive ventilation and cardiac management for Duchenne muscular dystrophy
Source: Eur Respir J 2006; 28: Suppl. 50, 184s
Year: 2006

Hypercapnic ventilatory response in patients with Steinert's myotonic dystrophy type 1
Source: Annual Congress 2013 –Clinical respiratory physiology in different diseases
Year: 2013

Risk factors for the need mechanical ventilatory support in patients with duchenne muscular dystrophy
Source: Annual Congress 2010 - Respiratory muscle function and training in acute and chronic respiratory disease
Year: 2010

Evolution of patients with myotonic dystrophy and home mechanical ventilation
Source: Eur Respir J 2007; 30: Suppl. 51, 316s
Year: 2007

Challenge already established: Identification of risk factors for early need for ventilatory support in Duchenne muscular dystrophy
Source: Annual Congress 2011 - Update on monitoring airway diseases
Year: 2011

Evaluating the effect of long-term idebenone treatment on respiratory morbidity in patients with Duchenne muscular dystrophy (DMD)
Source: International Congress 2019 – Rare and ultra-rare diseases and the lungs: updates and new perspectives
Year: 2019




Factors influencing compliance to long-term respiratory therapies in patients with myotonic dystrophy type 1
Source: International Congress 2017 – Noninvasive ventilation for chronic respiratory failure
Year: 2017

Nutritional status and admission risk in Duchenne muscular dystrophy (DMD)
Source: Annual Congress 2013 –Novel biomarkers and old parameters in clinical management of lung diseases
Year: 2013


Mechanical Ventilation (MV) in patients with Duchenne Muscular Dystrophy (DMD) in our area
Source: International Congress 2019 – Treatment of chronic respiratory failure with noninvasive ventilation
Year: 2019


Assesment for Sleep in Myotonic Dystrophy type 1(MD-1) patients
Source: International Congress 2018 – Obesity: comorbidities
Year: 2018

NIV in Duchenne Muscular Dystrophy : A qualitative study
Source: International Congress 2017 – Clinical and physiological challenges in noninvasive ventilation
Year: 2017

Introduction of domiciliary mechanical insufflation-exsufflation can reduce the incidence of crisis admissions in patients with Duchenne muscular dystrophy (DMD)
Source: Annual Congress 2012 - Current trends in home mechanical ventilation
Year: 2012


Ventilatory assistance in patients with Duchenne muscular dystrophy
Source: Eur Respir J 2006; 28: 468-469
Year: 2006


Age of loss of walking ability in patients with Duchenne muscular dystrophy: A marker for the elective use of mechanical ventilation?
Source: Annual Congress 2011 - Exercise tests and emerging outcomes: defining the impact of pulmonary rehabilitation
Year: 2011

Relationship between the respiratory function with motor functionality in Duchenne Mucular Dystrophy
Source: Virtual Congress 2020 – A knowledge update on respiratory muscle function, assessment and training
Year: 2020


The natural course of lung volumes in Duchenne Muscular Dystrophy (DMD)
Source: International Congress 2017 – Assessing the impact of respiratory and sleep problems in children
Year: 2017

The change of ventilation function in the patients of Duchenne muscular dystrophy under and beyond 12 years old and the effects of rehabilitation
Source: Eur Respir J 2007; 30: Suppl. 51, 766s
Year: 2007

Severe metabolic acidosis in chronically ventilated Duchenne muscular dystrophy patients
Source: Annual Congress 2011 - Mechanical ventilation and weaning
Year: 2011


The role of noninvasive ventilation in the management of type II respiratory failure in patients with myotonic dystrophy
Source: ERJ Open Res, 7 (3) 00192-2020; 10.1183/23120541.00192-2020
Year: 2021