Atypical presentation of a rare lung condition: axillary and paraspinal lymphadenopathy in a patient with clinical and radiological features of lymphangioleomatosis (LAM )

A. Kavidasan (London, United Kingdom), V. Taylor (London, United Kingdom), S. Chaudhry (London, United Kingdom), R. Siva (London, United Kingdom), Y. Raste (London, United Kingdom)

Source: International Congress 2018 – Pitfalls in the diagnosis and management of rare diffuse parenchymal lung diseases (DPLDs)
Disease area: Interstitial lung diseases, Respiratory infections

Congress or journal article abstract

Abstract

LAM is one of the rare cystic lung diseases usually found in women of childbering age group. Mediastinal and pelvic lymphadenopathy have been reported in many cases with LAM.

We present the first case with axillary and paraspinal lymphadenopathy in a patient with radiological featues of LAM.

Background: A 40 year old woman presented with gradually worsening breathlessnss over two years time. This was associated with cough and clear sputum production. There was no significant pastmedical or family hisory of note and the patient has had a healthy childhood. The patient is an ex-smoker with a five pack year history.

CXR

CT

Figure1

ALNB

MRI

Figure2

CTPET scan

Discussion



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A. Kavidasan (London, United Kingdom), V. Taylor (London, United Kingdom), S. Chaudhry (London, United Kingdom), R. Siva (London, United Kingdom), Y. Raste (London, United Kingdom). Atypical presentation of a rare lung condition: axillary and paraspinal lymphadenopathy in a patient with clinical and radiological features of lymphangioleomatosis (LAM ). 3032

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