e-learning
resources
Amsterdam 2015
Tuesday, 29.09.2015
Acute and chronic lung diseases: good clinical practice
Login
Search all ERS
e-learning
resources
Disease Areas
Airways Diseases
Interstitial Lung Diseases
Respiratory Critical Care
Respiratory Infections
Paediatric Respiratory Diseases
Pulmonary Vascular Diseases
Sleep and Breathing Disorders
Thoracic Oncology
Events
International Congress
Courses
Webinars
Conferences
Research Seminars
Journal Clubs
Publications
Breathe
Monograph
ERJ
ERJ Open Research
ERR
European Lung White Book
Handbook Series
Guidelines
All ERS guidelines
e-learning
CME Online
Case reports
Short Videos
SpirXpert
Procedure Videos
CME tests
Reference Database of Respiratory Sounds
Radiology Image Challenge
Brief tobacco interventions
EU Projects
VALUE-Dx
ERN-LUNG
ECRAID
UNITE4TB
Disease Areas
Events
Publications
Guidelines
e-learning
EU Projects
Login
Search
Pulmonary manifestations in patients with IgG4-related disease at a tertiary care institute
Lancelot Pinto (Mumbai, India), Radhika Banka, G.C. Yathish, C. Balakrishnan, Rohini Samant, Lancelot Pinto
Source:
International Congress 2015 – Acute and chronic lung diseases: good clinical practice
Session:
Acute and chronic lung diseases: good clinical practice
Session type:
Thematic Poster Session
Number:
3686
Disease area:
Interstitial lung diseases
Abstract
Background:IgG4-Related Disease(IgG4 RD)is a rare immune-mediated disease with multi-organ involvement.Aim:To describe pulmonary manifestations of patients with IgG4-RD.Methods:Chart review was performed of consecutive patients diagnosed with IgG4 RD between 2009-2014 at the PD Hinduja National Hospital,Mumbai.Included patients fulfilled diagnostic criteria of 'Disease Ministry of Health,Labor and Welfare,Japan.'Results:8 of 11 patients with IgG4 RD had pulmonary manifestations.Age of presentation ranged from 15-73 years.6 patients were female.Average delay in diagnosis was 9 months.Prior to diagnosis,3 patients received empiric antituberculous drugs and bronchoalveolar lavage performed in 3 patients was non-diagnostic.The right mainstem bronchus was found to be narrowed in 1 patient..Median IgG4 level was 4.76 mg/dl(IQR 3.26,6.1).Presenting symptoms,thoracic CT and hisptopathological findings are summarized
Feature(no of patients)
Symptoms
Fever(6) Cough(5) Shortness of breath(5) Weight loss(4) Stridor(1)
Thoracic CT findings (8 of 8 pts)
multiple small nodules< 1cm with an upper lobe predominance(5) ill defined patchy areas of consolidation(4) cervical and mediastinal homogeneously enhancing lymphadenopathy(4) ground glass opacities (3) peribronchial wall thickening(2) interlobular septal thickening(2) subglottic stenosis(2) mass-like lesion(1) bronchial stenosis(1)
Histopathological findings (4 of 8 pts)
subglottic biopsy(2)-non-diagnostic.Transbronchial lung biopsy(1)-Minimal interstitial fibrosis. Lymph node biopsy(1)-minimal inflammation and mild fibrosis.
Conclusion:Pulmonary involvement in IgG4 RD is common and should be sought for in patients diagnosed with the disease.
Rating:
You must
login
to grade this presentation.
Share or cite this content
Citations should be made in the following way:
Lancelot Pinto (Mumbai, India), Radhika Banka, G.C. Yathish, C. Balakrishnan, Rohini Samant, Lancelot Pinto. Pulmonary manifestations in patients with IgG4-related disease at a tertiary care institute. Eur Respir J 2015; 46: Suppl. 59, 3686
You must
login
to share this Presentation/Article on Twitter, Facebook, LinkedIn or by email.
Member's Comments
No comment yet.
You must
Login
to comment this presentation.
Related content which might interest you:
Late Breaking Abstract - Efficacy of Breathox® device inhalation on acute symptoms associated with COVID-19 (BREATH study)
Imaging of complicated pneumonia: what is new?
A 12-year-old male child with fever, productive cough and sudden onset paralysis
Related content which might interest you:
Pulmonary aspergillous; clinical features and outcomes in a tertiary care hospital
Source: International Congress 2015 – Immunodepression and severe pneumonia
Year: 2015
Pulmonary manifestations in adult patients with chronic granulomatous disease
Source: Annual Congress 2013 –Clinical management of orphan lung diseases
Year: 2013
Does the HLA-DRB1-genotype influence the course of disease in Danish sarcoidosis patients?
Source: Annual Congress 2013 –Sarcoidosis
Year: 2013
Clinical findings at initial presentation of IPF patients at a university hospital referral center
Source: International Congress 2014 – ILDs 5
Year: 2014
Respiratory manifestations in patients with systemic vasculitis with renal involvement in a tertiary hospital
Source: International Congress 2018 – Sarcoidosis, interstitial lung diseases and various clinical problems
Year: 2018
Prevalence of extra-pulmonary comorbidities in COPD patients and its correlation with severity of disease
Source: International Congress 2014 – Latest insights in chronic care
Year: 2014
Specific features of modern approach to management of patients with pulmonary sarcoidosis in Saint-Petersburg Sarcoidosis Center
Source: Eur Respir J 2007; 30: Suppl. 51, 84s
Year: 2007
Clinical characteristics of patients with Idiopathic pulmonary fibrosis in a tertiary care center of a developing country
Source: International Congress 2016 – ILD: from the bench to the bedside
Year: 2016
Pulmonary rehabilitation does not affect systemic inflammation in chronic obstructive pulmonary disease
Source: International Congress 2016 – Latest insights into pulmonary rehabilitation
Year: 2016
Idiopathic pulmonary fibrosis and systemic sclerosis-interstitial lung disease: features at admission to a tertiary pulmonology unit.
Source: Virtual Congress 2020 – Diagnostic and prognostic markers for disease-associated interstitial lung disease and hypersensitivity pneumonitis
Year: 2020
Clinical highlights from the 2011 ERS Congress in Amsterdam
Source: Eur Respir J 2012; 39: 1501-1510
Year: 2012
Association of pulmonary and cardiac manifestations in patients with primary antiphospholipid syndrome: A review of the Serbian national cohort study
Source: International Congress 2015 – Acute and chronic lung diseases: good clinical practice
Year: 2015
Subcutaneous sarcoidosis: A clinical analysis of nine patients
Source: International Congress 2015 – Sarcoidosis: clinical
Year: 2015
Clinical outcomes of patients with idiopathic pulmonary fibrosis in clinical practice: Follow-up results of the INSIGHTS-IPF registry
Source: International Congress 2015 – IPF: clinical aspects II
Year: 2015
Characteristics and outcomes of heritable pulmonary veno-occlusive disease due to EIF2AK4 mutations
Source: International Congress 2015 – Pulmonary hypertension: rare and hereditary causes of PAH
Year: 2015
Childhood pulmonary sarcoidosis
Source: Annual Congress 2013 –Sarcoidosis and other granulomatosis
Year: 2013
Pulmonary involvement in rheumatological diseases in children
Source: Virtual Congress 2021 – Paediatric bronchology
Year: 2021
Management of patients with idiopathic pulmonary fibrosis in clinical practice: the INSIGHTS-IPF registry
Source: Eur Respir J 2015; 46: 186-196
Year: 2015
Selected clinical highlights from the 2012 ERS congress in Vienna
Source: Eur Respir J 2013; 41: 1219-1227
Year: 2013
Ocular manifestations in unselected group of sarcoid patients hospitalised in the national tuberculosis and lung diseases research institute
Source: Eur Respir J 2002; 20: Suppl. 38, 435s
Year: 2002
We use cookies on our website to give you the most relevant experience by remembering your preferences and repeat visits. By clicking "Accept", you consent to the use of the cookies.
Accept