Intra-epithelial polymerization, accumulation and secretion of alpha1 antitrypsin (AAT) Z polymers in the lung of patients with alpha-1 antitrypsin deficiency (AATD)

L. Pini, L. Tiberio, M. S. Ludwig, N. Venkatesan, M. Bezzi, M. Novali, L. Corda, L. Schiaffonati, C. Tantucci (Brescia, Italy; Montrèal, Canada)

Source: Annual Congress 2010 - Epithelial cell biology
Session: Epithelial cell biology
Session type: Oral Presentation
Number: 1697
Disease area: Airway diseases

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L. Pini, L. Tiberio, M. S. Ludwig, N. Venkatesan, M. Bezzi, M. Novali, L. Corda, L. Schiaffonati, C. Tantucci (Brescia, Italy; Montrèal, Canada). Intra-epithelial polymerization, accumulation and secretion of alpha1 antitrypsin (AAT) Z polymers in the lung of patients with alpha-1 antitrypsin deficiency (AATD). Eur Respir J 2010; 36: Suppl. 54, 1697

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