New insights in rare diffuse parenchymal lung diseases (DPLDs) in adults and children

Poster Discussion
Chairs: M. Molina Molina (Hospitalet de Llobregat (Barcelona), Spain), R. Borie (Paris, France)
Prevalence of pleuroparenchymal fibroelastosis (PPFE): A retrospective single-centre case study
S. Geleff (Vienna, Austria), J. Gmeiner (Vienna, Austria), P. Jaksch (Vienna, Austria), H. Prosch (Vienna, Austria)
Congress or journal article abstractWebcastSlide presentationE-poster
Congress or journal article abstractWebcastSlide presentationE-poster
Clinical courses of asymptomatic patients with mild idiopathic pleuroparenchymal fibroelastosis
M. Toyoshima (Hamamatsu, Japan), A. Fukada (Hamamatsu, Japan), D. Akahori (Hamamatsu, Japan), T. Suda (Hamamatsu, Japan)
Congress or journal article abstract
Congress or journal article abstract
Traction bronchiectasis and platythorax on computed tomography are determinants of progression and mortality in pleuro-parenchymal fibroelastosis
P. George (London, United Kingdom), D. Armstrong-James (London, United Kingdom), A. Devaraj (London, United Kingdom), E. Renzoni (London, United Kingdom), T. Maher (London, United Kingdom), A. Wells (London, United Kingdom), I. Pulzato (London, United Kingdom), P. Molyneaux (London, United Kingdom), M. Kokosi (London, United Kingdom), V. Kouranos (London, United Kingdom), G. Margaritopoulos (London, United Kingdom), S. Desai (London, United Kingdom), F. Chua (London, United Kingdom)
Congress or journal article abstract
Congress or journal article abstract
Multidisciplinary team dedicated to suspected heritable pulmonary fibrosis
R. Borie (Paris, France), C. Kannengiesser (Paris, France), S. Amselem (Paris, France), O. Brugiere (Paris, France), D. Bouvry (Bobigny, France), A. Clement (Paris, France), V. Cottin (Lyon, France), P. Dieude (Paris, France), C. Dupin (Paris, France), R. Epaud (Creteil, France), L. Gouya (Paris, France), P. Fanen (Creteil, France), F. Sicre De Fontbrune (Paris, France), L. Wemeau-Stervinou (Lille, France), N. Nathan (Paris, France), B. Crestani (Paris, France)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Mid-term clinical course of the three Japanese SFTPC mutated familial interstitial pneumonia patients.
H. Ito (Nagasaki, Japan), H. Nakaoka (Nagasaki, Japan), Y. Yamashita (Nagasaki, Japan), M. Takaki (Nagasaki, Japan), T. Tanaka (Nagasaki, Japan), M. Ishida (Kochi, Japan), K. Morimoto (Nagasaki, Japan)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Functional assessment of newly identified SFTPA1 and SFTPA2 mutations in patients with idiopathic interstitial pneumonia (IIP) and lung cancer
N. Nathan (Paris, France), M. Legendre (Paris, France), E. Filhol-Blin (Paris, France), R. Borie (Paris, France), D. Bouvry (Bobigny, France), C. Kannengiesser (Paris, France), K. Ahmad (Lyon, France), J. Albuisson (Paris, France), N. Allou (Saint Denis de la Réunion, France), K. Borensztajn (Paris, France), A. Butt (Paris, France), B. Copin (Paris, France), V. Cottin (Lyon, France), B. Crestani (Paris, France), J. Dalphin (Besancon, France), F. Dastot Le Moal (Paris, France), C. Delacourt (Lyon, France), P. De Vuyst (Brussels, Belgium), P. Duquesnoy (Paris, France), V. Giraud (Boulogne Billancourt, France), C. Gomez (Marseille Billancourt, France), L. Gouya (Colombes Billancourt, France), V. Nau (Paris, France), H. Nunes (Bobigny, France), C. Picard (Suresnes, France), G. Prevot (Toulouse, France), P. Reix (Lyon, France), M. Reynaud-Gaubert (Marseille, France), J. Traclet (Lyon, France), A. Coulomb L'Hermine (Paris, France), A. Clement (Paris, France), S. Amselem (Paris, France)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
COPA syndrome restricted to life-threatening alveolar hemorrhages: clinical, pathological, molecular and biological characterization
N. Nathan (Paris, France), M. Legendre (Paris, France), S. Amselem (Paris, France), A. Clement (Paris, France), E. Filhol-Blin (Paris, France), N. Richard (Paris, France), S. Roullaud (Angoulême, France), M. Fayon (Bordeaux, France), G. Rice (Manchester, United Kingdom), D. Duffy (Paris, France), V. Bondet (Paris, France), A. Coulomb L’Hermine (Paris, France), B. Neven (Paris, France), M. Fremond (Paris, France), Y. Crow (Paris, France)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Down syndrome and pulmonary hemosiderosis: an under-recognized association
A. ALIMI (Paris, France), J. Taytard (Paris, France), R. Abou Taam (Paris, France), V. Houdouin (Paris, France), A. Forgeron (Le Mans, France), M. Lubrano Lavadera (Rouen, France), P. Cros (Brest, France), I. Gibertini (Tours, France), J. Derelle (Nancy, France), A. Deschildre (Lille, France), C. Thumerelle (Lille, France), R. Epaud (Créteil, France), P. Reix (Lyon, France), M. Fayon (Bordeaux, France), S. Roullaud (Angouleme, France), F. Troussier (Angers, France), M. Renoux (Montpellier, France), J. De Blic (Montpellier, France), S. Leyronnas (Paris, France), G. Thouvenin (Paris, France), C. Perisson (Paris, France), A. Ravel (Paris, France), A. Clément (Paris, France), H. Corvol (Paris, France), N. Nathan (Paris, France)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Exogenous lipoid pneumonia in African children: a mixed-methods case series
D. Marangu (Nairobi, Kenya), K. Pillay (Cape Town, South Africa), E. Banderker (Cape Town, South Africa), A. Vanker (Cape Town, South Africa), D. Gray (Cape Town, South Africa), M. Zampoli (Cape Town, South Africa)
Congress or journal article abstractWebcastSlide presentationE-poster
Congress or journal article abstractWebcastSlide presentationE-poster
Alveolar hemorrhage syndrome in children
A. Bogorad (Moscow, Russian Federation), Y. Mizernitsky (Moscow, Russian Federation), N. Rosinova (Moscow, Russian Federation), N. Lev (Moscow, Russian Federation), L. Sokolova (Moscow, Russian Federation), S. Djakova (Moscow, Russian Federation), I. Zorina (Moscow, Russian Federation), M. Kostiutchenko (Moscow, Russian Federation)
Congress or journal article abstractWebcastSlide presentationE-poster
Congress or journal article abstractWebcastSlide presentationE-poster
Effectiveness of inhibitor mTOR in patients with lymphangioleiomyomatosis.
L. Novikova (Saint-Petersburg, Russian Federation), M. Ilkovich (Saint-Petersburg, Russian Federation), D. Dzadzua, (Saint-Petersburg, Russian Federation), O. Baranova (Saint-Petersburg, Russian Federation), M. Vasilyeva (Saint-Petersburg, Russian Federation)
Congress or journal article abstractWebcastSlide presentationE-poster
Congress or journal article abstractWebcastSlide presentationE-poster
Pneumothorax in pulmonary langerhans cell histiocytosis (PLCH)
P. Le Guen (Paris, France), S. Chevret (Paris, France), E. Bugnet (Paris, France), C. De Margerie-Mellon (Paris, France), F. Jouenne (Paris, France), G. Lorillon (Paris, France), A. Seguin-Givelet (Paris, France), S. Mourah (Paris, France), D. Gossot (Paris, France), R. Vassallo (Rochester, United States of America), A. Tazi (Paris, France)
Congress or journal article abstractWebcastSlide presentationE-poster
Congress or journal article abstractWebcastSlide presentationE-poster
Cytokine profiling in Pulmonary Langerhans Cell Histiocytosis: novel insights into pathogenesis.
S. Barril Farre (Barcelona, Spain), S. Hortelano (Madrid, Spain), A. Luque (Madrid, Spain), M. Higueras (Madrid, Spain), C. Rodriguez-Martin (Madrid, Spain), C. Robledo (Madrid, Spain), A. Feliu (Barcelona, Spain), P. Millan (Barcelona, Spain), O. Sibila (Barcelona, Spain), F. Alonso (Madrid, Spain), D. Castillo (Barcelona, Spain)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Pleural effusion in patients with IgG4-related disease: new insights from a case series
O. Wand (Petah Tiqwa, Israel), O. Moreh Rahav (Petah Tiqwa, Israel), O. Shtraichman (Petah Tiqwa, Israel), M. Kramer (Petah Tiqwa, Israel)
Congress or journal article abstractWebcastSlide presentationE-poster
Congress or journal article abstractWebcastSlide presentationE-poster
Drug induced interstitial lung disease: a systematic review
S. Skeoch (Manchester, United Kingdom), N. Weatherley (Sheffield, United Kingdom), A. Swift (Sheffield, United Kingdom), A. Oldroyd (Manchester, United Kingdom), C. Johns (Sheffield, United Kingdom), C. Hayton (Manchester, United Kingdom), A. Giollo (Leeds, United Kingdom), J. Wild (Sheffield, United Kingdom), J. Waterton (Manchester, United Kingdom), M. Buch (Leeds, United Kingdom), K. Linton (Manchester, United Kingdom), I. Bruce (Manchester, United Kingdom), C. Leonard (Manchester, United Kingdom), B. Stephen (Sheffield, United Kingdom), N. Chaudhuri (Manchester, United Kingdom)
Congress or journal article abstract
Congress or journal article abstract
Unclassifiable interstitial lung disease: a distinct entity with heterogeneous progression
M. Nasser (Lyon, France), P. Rigaud (Lyon, France), K. Ahmad (Lyon, France), J. Traclet (Lyon, France), V. Cottin (Lyon, France)
Congress or journal article abstractWebcastSlide presentationE-poster
Congress or journal article abstractWebcastSlide presentationE-poster
Pulmonary Lymphangiomatosis – insights into an ultra-rare disease
N. Sarmand (Heidelberg, Germany), S. Piel (Heidelberg, Germany), E. Brunnemer (Heidelberg, Germany), J. Waelscher (Heidelberg, Germany), M. Polke (Heidelberg, Germany), A. Warth (Heidelberg, Germany), C. Heussel (Heidelberg, Germany), M. Eichinger (Heidelberg, Germany), F. Lasistschka (Heidelberg, Germany), B. Hoegerle (Heidelberg, Germany), L. Frankenstein (Heidelberg, Germany), H. Zabeck (Heidelberg, Germany), S. Rieken (Heidelberg, Germany), F. Herth (Heidelberg, Germany), M. Kreuter (Heidelberg, Germany)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation