Source: Eur Respir J 2010; 36: 311



Rating:

Share or cite this content

Citations should be made in the following way:
Bertrand J., Boucherle B., Billet A., Melin-Heschel P., Dannhoffer L., Vandebrouck C., Jayle C., Routaboul C., Molina M-C., Décout J-L., Becq F., Norez C.. Identification of a novel water-soluble activator of wild-type and F508del CFTR: GPact-11a. Eur Respir J 2010; 36: 311

Member's Comments

No comment yet.

Related content which might interest you: Improved CFTR and lung function with VX-770, a novel investigational potentiator of CFTR, in subjects with the G551D-CFTR mutation Source: Annual Congress 2010 - Cystic fibrosis: new targets for therapy and impact of viral infections Year: 2010 Rescue of mutant ABCA3 by small molecular correctors Source: International Congress 2017 – Lung fibrosis: basic science Year: 2017 Targeting a genetic defect: cystic fibrosis transmembrane conductance regulator modulators in cystic fibrosis Source: Eur Respir Rev 2013; 22: 58-65 Year: 2013 Clinical development of triple-combination CFTR modulators for cystic fibrosis patients with one or two F508del alleles Source: ERJ Open Res, 5 (2) 00082-2019; 10.1183/23120541.00082-2019 Year: 2019 Evaluation of MRP1-5 gene expression in cystic fibrosis patients homozygous for the ΔF508 mutation Source: Annual Congress 2003 - Cystic fibrosis: new genes, new controversies Year: 2003 Ivacaftor treatment in patients with cystic fibrosis and the G551D-CFTR mutation Source: Eur Respir Rev 2013; 22: 66-71 Year: 2013 Identification of a new cystic fibrosis transmembrane regulator mutation in a severely affected patient Source: Eur Respir J 2002; 19: 374-376 Year: 2002 Novel insights into surfactant protein C trafficking revealed through the study of a pathogenic mutant Source: Eur Respir J, 59 (1) 2100267; 10.1183/13993003.00267-2021 Year: 2022 A novel CFTR mutation found in a Chinese cystic fibrosis patient Source: Eur Respir J 2005; 26: Suppl. 49, 402s Year: 2005 Rescue of multiple class II CFTR mutations by elexacaftor+tezacaftor+ivacaftor mediated in part by the dual activities of elexacaftor as both corrector and potentiator Source: Eur Respir J, 57 (6) 2002774; 10.1183/13993003.02774-2020 Year: 2021 Analysis of CFTR gene mutations in 24 Japanese individuals with cystic fibrosis Source: Annual Congress 2010 - Cystic fibrosis: lung disease infection and more Year: 2010 ENaC inhibition in cystic fibrosis: potential role in the new era of CFTR modulator therapies Source: Eur Respir J, 56 (6) 2000946; 10.1183/13993003.00946-2020 Year: 2020 Rescue of CFTR function impaired by mutations in exon 15 Source: Virtual Congress 2020 – Clinical monitoring and new therapies for cystic fibrosis Year: 2020 Chronic ataluren (PTC124) treatment of nonsense mutation cystic fibrosis Source: Eur Respir J 2011; 37: 59-69 Year: 2011 Genotypic diversity of Pseudomonas aeruginosa in cystic fibrosis patients with the CFTR I1234V mutation in a large kindred family Source: Annual Congress 2012 - Cystic fibrosis (adults and children): risk factors and clinical problems Year: 2012 A three miRNA signature regulates the CF transmembrane conductance regulator (CFTR) in cystic fibrosis airway epithelium Source: Annual Congress 2011 - Epithelial cells: role in health and disease Year: 2011 Analysis of CFTR function in human monocytes Source: Annual Congress 2010 - Cystic fibrosis: lung disease and much more Year: 2010