Severe pulmonary hypertension in histiocytosis X: long-term improvement with bosentan

Kiakouama L., Cottin V., Etienne-mastroianni B., Khouatra C., Humbert M., Cordier J.F.

Source: Eur Respir J 2010; 36: 202-204
Journal Issue: July
Disease area: Pulmonary vascular diseases

Full text journal articlePDF journal article, handout or slides

Rating: 0
You must login to grade this presentation.

Share or cite this content

Citations should be made in the following way:
Kiakouama L., Cottin V., Etienne-mastroianni B., Khouatra C., Humbert M., Cordier J.F.. Severe pulmonary hypertension in histiocytosis X: long-term improvement with bosentan. Eur Respir J 2010; 36: 202-204

You must login to share this Presentation/Article on Twitter, Facebook, LinkedIn or by email.

Member's Comments

No comment yet.
You must Login to comment this presentation.


Related content which might interest you:
Clinical study of pulmonary hypertension complicating pulmonary Langerhans cell histiocytosis
Source: Annual Congress 2012 - Diffuse parenchymal lung disease I
Year: 2012

Long-term outcome of sarcoidosis-associated pulmonary hypertension in the modern treatment era
Source: International Congress 2015 – Pulmonary hypertension: new treatment insights
Year: 2015

Pulmonary hypertension in pulmonary Langerhans’ cell histiocytosis
Source: Eur Respir Mon 2012; 57: 161-165
Year: 2012


Pathological findings in histiocytosis X with pulmonary hypertension
Source: Annual Congress 2012 - Diffuse parenchymal lung disease IV
Year: 2012

RISE-IIP: Riociguat for the treatment of pulmonary hypertension associated with idiopathic interstitial pneumonia
Source: International Congress 2017 – New insights into pulmonary hypertension from recent trials
Year: 2017




Pulmonary hypertension associated with sarcoidosis and experience of treatment with pentoxifylline (Vasonite)
Source: Eur Respir J 2006; 28: Suppl. 50, 426s
Year: 2006

Treatment of early systemic sclerosis associated pulmonary arterial hypertension with endothelin receptor antagonists improves survival
Source: Annual Congress 2007 - Clinical aspects of pulmonary arterial hypertension
Year: 2007



Management and long-term outcomes of sarcoidosis-associated pulmonary hypertension
Source: Eur Respir J, 50 (4) 1700465; 10.1183/13993003.00465-2017
Year: 2017



Chronic thrombo-embolic pulmonary hypertension: Long-term outcomes in operated and non-operated patients
Source: International Congress 2016 – Pulmonary hypertension and chronic thromboembolic pulmonary hypertension
Year: 2016

Pulmonary hypertension in orphan lung diseases
Source: Eur Respir Mon 2011; 54: 317-331
Year: 2011


Pulmonary hypertension in patients with chronic myeloproliferative disorders
Source: Eur Respir J 2010; 35: 1396-1406
Year: 2010



Pulmonary hypertension associated with sarcoidosis
Source: Eur Respir Mon 2012; 57: 166-181
Year: 2012


IgG4-related disease in pulmonary arterial hypertension on long-term epoprostenol treatment
Source: Eur Respir J 2014; 43: 1516-1519
Year: 2014


Efficacy and safety of oral bosentan in patients with Down‘s syndrome and pulmonary arterial hypertension due to congenital heart disease
Source: Annual Congress 2012 - Pulmonary circulation: clinical aspects of PAH and associated PH
Year: 2012

Long-term efficacy of bosentan in treatment of pulmonary arterial hypertension in children
Source: Eur Respir J 2011; 37: 70-77
Year: 2011



Long-term safety of a new formulation of epoprostenol in pulmonary arterial hypertension
Source: Annual Congress 2013 –Pulmonary circulation: clinical diagnosis, imaging, biomarkers and treatment
Year: 2013

Long-term effects of bosentan in patients with HIV-associated pulmonary arterial hypertension
Source: Eur Respir J 2009; 33: 92-98
Year: 2009



Treatment with sildenafil for pulmonary hypertension in pulmonary fibrosis
Source: Eur Respir J 2005; 26: Suppl. 49, 562s
Year: 2005

Treatment of severe pulmonary hypertension in patients with interstitial lung disease: Results in 72 patients from the “HYPID” prospective study
Source: Annual Congress 2013 –Pulmonary circulation: treatment
Year: 2013

Effects of bosentan in patients with severe pulmonary hypertension and mild-to-moderate COPD
Source: Annual Congress 2009 - Pulmonary circulation I
Year: 2009