Cystic fibrosis transmembrane conductance regulator pharmacotherapy

L.J.V. Galietta

Source: Eur Respir Mon; 2006: 35: 88–104
Journal Issue: Cystic Fibrosis
Disease area: Airway diseases, Paediatric lung diseases

PDF journal article, handout or slides

Rating: 0
You must login to grade this presentation.

Share or cite this content

Citations should be made in the following way:
L.J.V. Galietta. Cystic fibrosis transmembrane conductance regulator pharmacotherapy. Eur Respir Mon; 2006: 35: 88–104

You must login to share this Presentation/Article on Twitter, Facebook, LinkedIn or by email.

Member's Comments

No comment yet.
You must Login to comment this presentation.


Related content which might interest you:
Channelopathies in bronchiectasis
Source: Eur Respir Mon 2011; 52: 150-162
Year: 2011


Atypical cystic fibrosis
Source: ISSN=ISSN 1025-448x, ISBN=ISBN 1-904097-46-6, page=38
Year: 2006

Targeting a genetic defect: cystic fibrosis transmembrane conductance regulator modulators in cystic fibrosis
Source: Eur Respir Rev 2013; 22: 58-65
Year: 2013



Cigarette smoke induces systemic defects in cystic fibrosis transmembrane conductance regulator (CFTR) ion transport
Source: Annual Congress 2013 –Cystic fibrosis: basic and applied science
Year: 2013

Pharmacological treatment of the biochemical defect in cystic fibrosis airways
Source: Eur Respir J 2001; 17: 1314-1321
Year: 2001



A three miRNA signature regulates the CF transmembrane conductance regulator (CFTR) in cystic fibrosis airway epithelium
Source: Annual Congress 2011 - Epithelial cells: role in health and disease
Year: 2011

The cystic fibrosis transmembrane conductance regulator: state of the art
Source: Breathe 2008; 5: 163-167
Year: 2008

Expression and function of cystic fibrosis transmembrane conductance regulator in rat intrapulmonary arteries
Source: Eur Respir J 2007; 30: 857-864
Year: 2007



Cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID)
Source: Breathe, 17 (3) 210088; 10.1183/20734735.0088-2021
Year: 2021



Cystic fibrosis and survival to 40 years: a study of cystic fibrosis transmembrane conductance regulator function
Source: Eur Respir J 2011; 37: 1076-1082
Year: 2011



Identification of a new cystic fibrosis transmembrane regulator mutation in a severely affected patient
Source: Eur Respir J 2002; 19: 374-376
Year: 2002



The cystic fibrosis transmembrane conductance regulator and its modulators: clinical implications
Source: Virtual Congress 2020 – Respiratory infections
Year: 2020


LATE-BREAKING ABSTRACT: Reducing inflammation in the lung by targeting the endothelial cystic fibrosis transmembrane conductance regulator with copper-tobramycin
Source: International Congress 2014 – Cystic fibrosis: genotypes, inflammation and microbiology
Year: 2014

Inflammation in cystic fibrosis airways: relationship to increased bacterial adherence
Source: Eur Respir J 2001; 17: 27-35
Year: 2001



Cystic fibrosis: to ion transport and beyond
Source: Eur Respir J 2010; 36: 991-992
Year: 2010


CFTR: cystic fibrosis and beyond
Source: Eur Respir J 2014; 44: 1042-1054
Year: 2014



How organoids helped to discover cystic fibrosis transmembrane conductance regulator (CFTR) therapeutics and predict response to treatment
Source: International Congress 2016 – Closing the gap: novel translational research strategies
Year: 2016


Cross-talk of inflammatory mediators and airway epithelium reveals the cystic fibrosis transmembrane conductance regulator as a major target
Source: ERJ Open Res, 7 (4) 00247-2021; 10.1183/23120541.00247-2021
Year: 2021



New insights into the pathophysiology of lung disease in cystic fibrosis patients
Source: ISSN=ISSN 1025-448x, ISBN=ISBN 1-904097-46-6, page=1
Year: 2006

Lung function, weight, and sweat chloride responses in patients with cystic fibrosis and the G551D-CFTR mutation treated with ivacaftor: A secondary analysis
Source: Annual Congress 2013 –Cystic fibrosis: lung function and change of lung function in infants and children before and after treatment
Year: 2013