The effect of alpha-1 antitrypsin (AAT) augmentation therapy on the liver phenotype in individuals with homozygous Pi*Z AAT mutation (genotype Pi*ZZ)

M. Fromme (Aachen, Germany), K. Hamesch (Aachen, Germany), C. Schneider (Aachen, Germany), M. Mandorfer (Vienna, Austria), K. Holtz-Thorhauge (Odense, Denmark), V. Pereira (Funchal, Portugal), M. Pons (Barcelona, Spain), M. Reichert (Homburg, Germany), S. Amzou (Aachen, Germany), R. Bals (Homburg, Germany), R. Koczulla (Marburg, Germany), M. Miravitlles (Barcelona, Spain), S. Janciauskiene (Hannover, Germany), J. Genesca (Barcelona, Spain), F. Benini (Brescia, Italy), J. Chorostowska-Wynimko (Warsaw, Poland), W. Griffiths (Cambridge, United Kingdom), E. Aigner (Salzburg, Austria), A. Teumer (Greifswald, Germany), M. Trauner (Vienna, Austria), A. Krag (Odense, Denmark), C. Trautwein (Aachen, Germany), P. Strnad (Aachen, Germany)

Source: International Congress 2022 – Alpha-1 antitrypsin deficiency and chronic airway obstructive diseases
Session: Alpha-1 antitrypsin deficiency and chronic airway obstructive diseases
Session type: Thematic Poster
Number: 2430

Congress or journal article abstractE-poster

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Citations should be made in the following way:
M. Fromme (Aachen, Germany), K. Hamesch (Aachen, Germany), C. Schneider (Aachen, Germany), M. Mandorfer (Vienna, Austria), K. Holtz-Thorhauge (Odense, Denmark), V. Pereira (Funchal, Portugal), M. Pons (Barcelona, Spain), M. Reichert (Homburg, Germany), S. Amzou (Aachen, Germany), R. Bals (Homburg, Germany), R. Koczulla (Marburg, Germany), M. Miravitlles (Barcelona, Spain), S. Janciauskiene (Hannover, Germany), J. Genesca (Barcelona, Spain), F. Benini (Brescia, Italy), J. Chorostowska-Wynimko (Warsaw, Poland), W. Griffiths (Cambridge, United Kingdom), E. Aigner (Salzburg, Austria), A. Teumer (Greifswald, Germany), M. Trauner (Vienna, Austria), A. Krag (Odense, Denmark), C. Trautwein (Aachen, Germany), P. Strnad (Aachen, Germany). The effect of alpha-1 antitrypsin (AAT) augmentation therapy on the liver phenotype in individuals with homozygous Pi*Z AAT mutation (genotype Pi*ZZ). 2430

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