Haemodynamically proven pulmonary hypertension in a patient with GATA2 deficiency-associated pulmonary alveolar proteinosis and fibrosis

Stéphane Jouneau, Alice Ballerie, Mallorie Kerjouan, Xavier Demant, Elodie Blanchard, Mathieu Lederlin

Source: Eur Respir J, 49 (5) 1700407; 10.1183/13993003.00407-2017
Journal Issue: May
Disease area: Interstitial lung diseases, Pulmonary vascular diseases

Congress or journal article abstractFull text journal articlePDF journal article, handout or slides

Rating: 0
You must login to grade this presentation.

Share or cite this content

Citations should be made in the following way:
Stéphane Jouneau, Alice Ballerie, Mallorie Kerjouan, Xavier Demant, Elodie Blanchard, Mathieu Lederlin. Haemodynamically proven pulmonary hypertension in a patient with GATA2 deficiency-associated pulmonary alveolar proteinosis and fibrosis. Eur Respir J, 49 (5) 1700407; 10.1183/13993003.00407-2017

You must login to share this Presentation/Article on Twitter, Facebook, LinkedIn or by email.

Member's Comments

No comment yet.
You must Login to comment this presentation.


Related content which might interest you:
Pulmonary alveolar proteinosis and idiopathic pulmonary hemosiderosis
Source: International Congress 2019 – CCC Airway diseases
Year: 2019



Association of pulmonary alveolar proteinosis and fibrosis: patient with GATA2 deficiency
Source: Eur Respir J 2016; 48: 1510-1514
Year: 2016


Pulmonary hypertension in patients with idiopathic pulmonary fibrosis
Source: Eur Respir Mon 2012; 57: 148-160
Year: 2012


The impact of emphysema in pulmonary fibrosis
Source: Eur Respir Rev 2013; 22: 153-157
Year: 2013



Pulmonary hypertension in patients with idiopathic pulmonary fibrosis and combined pulmonary fibrosis and emphysema: hemodynamic severity
Source: International Congress 2018 – Pulmonary hypertension in lung diseases and the role of the right ventricle
Year: 2018

Combined pulmonary fibrosis and emphysema: a distinct underrecognised entity
Source: Eur Respir J 2005; 26: 586-593
Year: 2005



Pulmonary hypertension in idiopathic pulmonary fibrosis
Source: Annual Congress 2010 - Clinical aspects in pulmonary fibrosis
Year: 2010

Diffuse pulmonary fibrosis and pulmonary emphysema associated with paradoxically normal spirometry
Source: Eur Respir J 2006; 28: Suppl. 50, 100s
Year: 2006

Our cases with pulmonary alveolar proteinosis
Source: International Congress 2018 – Pitfalls in the diagnosis and management of rare diffuse parenchymal lung diseases (DPLDs)
Year: 2018

Subtypes of pulmonary emphysema on HRCT affect prognosis on combined pulmonary fibrosis and emphysema in idiopathic pulmonary fibrosis
Source: Annual Congress 2013 –Idiopathic pulmonary fibrosis: clinical view
Year: 2013


The role of apoptosis in idiopathic pulmonary alveolar proteinosis
Source: Annual Congress 2006 - Usefulness of broncoalveolar lavage (BAL) in interstitial lung diseases
Year: 2006


Pulmonary arterial hypertension in combined pulmonary emphysema and fibrosis
Source: Annual Congress 2005 - Pulmonary arterial hypertension diagnosis and therapy
Year: 2005


Occult alveolar haemorrhage in pulmonary veno-occlusive disease
Source: Eur Respir J 2006; 27: 108-113
Year: 2006



Abnormal pulmonary arterial remodelling in patients with combined pulmonary fibrosis emphysema (CPFE) and idiopathic pulmonary fibrosis (IPF)
Source: Annual Congress 2011 - Clinical approach of diffuse parenchymal lung disease
Year: 2011

Coexistent pulmonary emphysema delays the decrease in vital capacity in patients with idiopathic pulmonary fibrosis
Source: Annual Congress 2008 - Miscellaneous aspects of interstitial lung disease
Year: 2008


Pulmonary vascular changes in COPD and idiopathic pulmonary fibrosis (IPF)
Source: Annual Congress 2006 - Clinical physiology
Year: 2006

VEGF expression does not differentiate between idiopathic pulmonary fibrosis and pulmonary sarcoidosis
Source: Eur Respir J 2007; 30: Suppl. 51, 574s
Year: 2007

Pulmonary hypertension is common in end-stage sarcoidosis
Source: Annual Congress 2005 - Progresses in granolomatous lung disease
Year: 2005


Titrated oxygen requirement and prognostication in idiopathic pulmonary fibrosis
Source: Eur Respir J 2012; 39: 359-365
Year: 2012