“Chronic ataluren (PTC124) treatment of nonsense mutation cystic fibrosis.” M. Wilschanski, L.L. Miller, D. Shoseyov, H. Blau, J. Rivlin, M. Aviram, M. Cohen, S. Armoni, Y. Yaakov, T. Pugatch, M. Cohen-Cymberknoh, N.L. Miller, A. Reha, V.J. Northcutt, S. Hirawat, K. Donnelly, G.L. Elfring, T. Ajayi and E. Kerem. Eur Respir J 2011; 38: 59–69.
Source: Eur Respir J 2011; 38: 996
Rating:
You must login to grade this presentation.
Share or cite this content
Citations should be made in the following way:
“Chronic ataluren (PTC124) treatment of nonsense mutation cystic fibrosis.” M. Wilschanski, L.L. Miller, D. Shoseyov, H. Blau, J. Rivlin, M. Aviram, M. Cohen, S. Armoni, Y. Yaakov, T. Pugatch, M. Cohen-Cymberknoh, N.L. Miller, A. Reha, V.J. Northcutt, S. Hirawat, K. Donnelly, G.L. Elfring, T. Ajayi and E. Kerem. Eur Respir J 2011; 38: 59–69.. Eur Respir J 2011; 38: 996
You must login to share this Presentation/Article on Twitter, Facebook, LinkedIn or by email.
Member's Comments
Related content which might interest you:
Related content which might interest you:
Author Correction: “Interferon-gamma release assays for the diagnosis of active tuberculosis: a systematic review and meta-analysis.” M. Sester, G. Sotgiu, C. Lange, C. Giehl, E. Girardi, G.B. Migliori, A. Bossink, K. Dheda, R. Diel, J. Dominguez, M. Lipman, J. Nemeth, P. Ravn, S. Winkler, E. Huitric, A. Sandgren and D. Manissero. Eur Respir J 2011; 37: 100–111. Source: Eur Respir J 2012; 39: 793 Year: 2012
“Effect of different asthma treatments on risk of cold-related exacerbations.” H.K. Reddel, C. Jenkins, S. Quirce, M.R. Sears, E.D. Bateman, P.M. O'Byrne, M. Humbert, R. Buhl, T. Harrison, G.G. Brusselle, A. Thorén, U. Sjöbring, S. Peterson, O. Östlund and G.S. Eriksson. Eur Respir J 2011; 38: 584–593. Source: Eur Respir J 2012; 39: 1280 Year: 2012
Author Correction: “Interferon-gamma release assays for the diagnosis of latent Mycobacterium tuberculosis infection: a systematic review and meta-analysis.” R. Diel, D. Goletti, G. Ferrara, G. Bothamley, D. Cirillo, B. Kampmann, C. Lange, M. Losi, R. Markova, G.B. Migliori, A. Nienhaus, M. Ruhwald, D. Wagner, J.P. Zellweger, E. Huitric, A. Sandgren and D. Manissero. Eur Respir J 2011; 37: 88–99. Source: Eur Respir J 2012; 39: 793 Year: 2012
"No evidence for interstitial lung oedema by extensive pulmonary function testing at 4,559". C. Dehnert, A.M. Luks, G. Schendler, E. Menold, M.M. Berger, H. Mairbäurl, V. Faoro, D.M. Bailey, C. Castell, G. Hahn, P. Vock, E.R. Swenson and P. Bärtsch. Eur Respir J 2010; 35: 812-820. Source: Eur Respir J 2010; 36: 699 Year: 2010
“Periostin, a matrix protein, is a novel biomarker for idiopathic interstitial pneumonias.” M. Okamoto, T. Hoshino, Y. Kitasato, Y. Sakazaki, T. Kawayama, K. Fujimoto, K. Ohshima, H. Shiraishi, M. Uchida, J. Ono, S. Ohta, S. Kato, K. Izuhara and H. Aizawa. Eur Respir J 2011; 37: 1119–1127. Source: Eur Respir J 2014; 44: 826 Year: 2014
“Mast cells promote lung vascular remodelling in pulmonary hypertension.” J. Hoffmann, J. Yin, M. Kukucka, N. Yin, I. Saarikko, A. Sterner-Kock, H. Fujii, H. Leong-Poi, H. Kuppe, R.T. Schermuly and W.M. Kuebler. Eur Respir J 2011; 37: 1400–1410. Source: Eur Respir J 2012; 40: 515-517 Year: 2012
Author Correction: “Rhinovirus induces MUC5AC in a human infection model and in vitro via NF-?B and EGFR pathways.” C.A. Hewson, J.J. Haas, N.W. Bartlett, S.D. Message, V. Laza-Stanca, T. Kebadze, G. Caramori, J. Zhu, M.R. Edbrooke, L.A. Stanciu, O.M. Kon, A. Papi, P.K. Jeffery, M.R. Edwards and S.L. Johnston. Eur Respir J 2010; 36: 1425–1435. Source: Eur Respir J 2012; 39: 793 Year: 2012
“Sleep apnoea is associated with major cardiac events in peripheral arterial disease.” Karri T. Utriainen, Juhani K. Airaksinen, Olli Polo, Ruut Laitio, Mikko J. Pietilä, Harry Scheinin, Tero Vahlberg, Kari A. Leino, Erkki S. Kentala, Jouko R. Jalonen, Harri Hakovirta, Riitta Parkkola, Sami Virtanen and Timo T. Laitio. Eur Respir J 2014; 43: 1652-1660. Source: Eur Respir J, 51 (4) 1351309; 10.1183/13993003.51309-2013 Year: 2018
“Blood basophil activation is a reliable biomarker of allergic bronchopulmonary aspergillosis in cystic fibrosis.” Yael Gernez, Jeffrey Waters, Bojana Mirkovic, Gillian M. Lavelle, Colleen E. Dunn, Zoe A. Davies, Cassie Everson, Rabindra Tirouvanziam, Elana Silver, Sylvan Wallenstein, Sanjay H. Chotirmall, Noel G. McElvaney, Leonore A. Herzenberg and Richard B. Moss. Eur Respir J 2016; 47: 177–185. Source: Eur Respir J 2016; 47:1892 Year: 2016
“Detection of SV40 like viral DNA and viral antigens in malignant pleural mesothelioma.” M. Ramael, J. Nagels, H. Heylen, S. De Schepper, J. Paulussen, M. De Maeyer and C. Van Haesendonck. Eur Respir J 1999; 14: 1381–1386. Source: Eur Respir J, 55 (5) 9951381; 10.1183/13993003.51381-1999 Year: 2020
“Drivers of year-to-year variation in exacerbation frequency of COPD: analysis of the AERIS cohort” Tom M.A. Wilkinson, Emmanuel Aris, Simon C. Bourne, Stuart C. Clarke, Mathieu Peeters, Thierry G. Pascal, Laura Taddei, Andrew C. Tuck, Viktoriya L. Kim, Kristoffer K. Ostridge, Karl J. Staples, Nicholas P. Williams, Anthony P. Williams, Stephen A. Wootton and Jeanne-Marie Devaster, on behalf of the AERIS Study Group. ERJ Open Res 2019; 5: 00248-2018. Source: ERJ Open Res, 5 (3) 00248-2018-AUT; 10.1183/23120541.50248-2018 Year: 2019
Withdrawal notice for: “Circulating RNA differences between patients with stable and progressive lung function in IPF.” Britt Clynick, Helen E. Jo, Tamera J. Corte, Ian N. Glaspole, Christopher Grainge, Peter M.A. Hopkins, Paul N. Reynolds, Sally Chapman, E. Haydn Walters, Christopher Zappala, Gregory J. Keir, Wendy A. Cooper, Annabelle M. Mahar, Samantha Ellis, Nicole Goh, Svetlana Baltic, Marissa Ryan, Dino Tan and Yuben Moodley. Eur Respir J 2019; in press. Source: Eur Respir J, 54 (5) 1802115; 10.1183/13993003.02115-2018 Year: 2019
“Global strategy for asthma management and prevention: GINA executive summary.” E.D. Bateman, S.S. Hurd, P.J. Barnes, J. Bousquet, J.M. Drazen, J.M. FitzGerald, P. Gibson, K. Ohta, P. O'Byrne, S.E. Pedersen, E. Pizzichini, S.D. Sullivan, S.E. Wenzel and H.J. Zar. Eur Respir J 2008; 31: 143–178. Source: Eur Respir J, 51 (2) 0751387; 10.1183/13993003.51387-2007 Year: 2018
“Cellular mechanisms underlying steroid-resistant asthma.” Ridhima Wadhwa, Kamal Dua, Ian M. Adcock, Jay C. Horvat, Richard Y. Kim and Philip M. Hansbro. Eur Respir Rev 2019; 28: 190021. Source: Eur Respir Rev, 28 (154) 195096; 10.1183/16000617.5096-2019 Year: 2019
“Safety of nintedanib added to pirfenidone treatment for idiopathic pulmonary fibrosis.” Kevin R. Flaherty, Charlene D. Fell, J. Terrill Huggins, Hilario Nunes, Robert Sussman, Claudia Valenzuela, Ute Petzinger, John L. Stauffer, Frank Gilberg, Monica Bengus and Marlies Wijsenbeek. Eur Respir J 2018; 52: 1800230. Source: Eur Respir J, 52 (4) 1850230; 10.1183/13993003.50230-2018 Year: 2018
“Characterisation of patients with interstitial pneumonia with autoimmune features.” Justin M. Oldham, Ayodeji Adegunsoye, Eleanor Valenzi, Cathryn Lee, Leah Witt, Lena Chen, Aliya N. Husain, Steven Montner, Jonathan H. Chung, Vincent Cottin, Aryeh Fischer, Imre Noth, Rekha Vij and Mary E. Strek. Eur Respir J 2016; 47: 1767–1775. Source: Eur Respir J, 49 (5) 1551565; 10.1183/13993003.51565-2015 Year: 2017
“Prospective validation of the RAPID clinical risk prediction score in adult patients with pleural infection: the PILOT study.” John P. Corcoran, Ioannis Psallidas, Stephen Gerry, Francesco Piccolo, Coenraad F. Koegelenberg, Tarek Saba, Cyrus Daneshvar, Ian Fairbairn, Richard Heinink, Alex West, Andrew E. Stanton, Jayne Holme, Jack A. Kastelik, Henry Steer, Nicola J. Downer, Mohammed Haris, Emma H. Baker, Caroline F. Everett, Justin Pepperell, Thomas Bewick, Lonny Yarmus, Fabien Maldonado, Burhan Khan, Alan Hart-Thomas, Georgina Hands, Geoffrey Warwick, Duneesha De Fonseka, Maged Hassan, Mohammed Munavvar, Anur Guhan, Mitra Shahidi, Zara Pogson, Lee Dowson, Natalia D. Popowicz, Judith Saba, Neil R. Ward, Rob J. Hallifax, Melissa Dobson, Rachel Shaw, Emma L. Hedley, Assunta Sabia, Barbara Robinson, Gary S. Collins, Helen E. Davies, Ly-Mee Yu, Robert F. Miller, Nick A. Maskell and Najib M. Rahman. Eur Respir J 2020; 56: 2000130. Source: Eur Respir J, 56 (6) 2050130; 10.1183/13993003.50130-2020 Year: 2020
“International ERS/ATS guidelines on definition, evaluation and treatment of severe asthma.” Kian Fan Chung, Sally E. Wenzel, Jan L. Brozek, Andrew Bush, Mario Castro, Peter J. Sterk, Ian M. Adcock, Eric D. Bateman, Elisabeth H. Bel, Eugene R. Bleecker, Louis-Philippe Boulet, Christopher Brightling, Pascal Chanez, Sven-Erik Dahlen, Ratko Djukanovic, Urs Frey, Mina Gaga, Peter Gibson, Qutayba Hamid, Nizar N. Jajour, Thais Mauad, Ronald L. Sorkness and W. Gerald Teague. Eur Respir J 2014; 43: 343–373. Source: Eur Respir J, 52 (1) 1352020; 10.1183/13993003.52020-2013 Year: 2018
“International ERS/ATS guidelines on definition, evaluation and treatment of severe asthma.” Kian Fan Chung, Sally E. Wenzel, Jan L. Brozek, Andrew Bush, Mario Castro, Peter J. Sterk, Ian M. Adcock, Eric D. Bateman, Elisabeth H. Bel, Eugene R. Bleecker, Louis-Philippe Boulet, Christopher Brightling, Pascal Chanez, Sven-Erik Dahlen, Ratko Djukanovic, Urs Frey, Mina Gaga, Peter Gibson, Qutayba Hamid, Nizar N. Jajour, Thais Mauad, Ronald L. Sorkness and W. Gerald Teague. Eur Respir J 2014; 43: 343–373. Source: Eur Respir J 2014; 43: 1216 Year: 2014
“The effect of exacerbation history on outcomes in the IMPACT trial.” David M.G. Halpin, Mark T. Dransfield, MeiLan K. Han, C. Elaine Jones, Sally Kilbride, Peter Lange, David A. Lipson, David A. Lomas, Fernando J. Martinez, Steve Pascoe, Dave Singh, Robert Wise and Gerard J. Criner. Eur Respir J 2020; 55: 1901921. Source: Eur Respir J, 55 (6) 1951921; 10.1183/13993003.51921-2019 Year: 2020