European Respiratory Society Monograph, Vol. 86. 2019
ISBN (electronic): 978-1-84984-112-2
DOI: 10.1183/2312508X.erm8619
Interest in interstitial lung diseases (ILDs) has risen in recent years. A large volume of basic and clinical research has increased our understanding of the pathogenesis of idiopathic pulmonary fibrosis (IPF) and non-IPF fibrotic ILDs. The ILD field is now evolving rapidly, with major implications for practical management. This Monograph provides expert clinical guidance on these difficult diseases, which will be helpful to both respiratory and nonrespiratory physicians alike. The initial chapters consider diagnostic issues, pulmonary function tests and techniques that are currently in development. The book then goes on to cover a variety of pulmonary manifestations of very different disease entities, such as connective tissue diseases, systemic vasculitis and much more.
Preface John R. Hurst Eur Respir Monogr 2019; 86: v |  |
Guest Editors
Eur Respir Monogr 2019; 86: vi-viii |  |
Introduction Wim A. Wuyts, Vincent Cottin, Paolo Spagnolo, Athol U. Wells Eur Respir Monogr 2019; 86: ix-xii |   |
List of abbreviations
Eur Respir Monogr 2019; 86: xiv |  |
Multidisciplinary approach to systemic diseases: benefits for diagnosis and management of complex disorders Fabrizio Luppi, Paola Faverio, Wim A. Wuyts Eur Respir Monogr 2019; 86: 1-13 |   |
Pulmonary function tests in multisystem disorders: prejudices and pitfalls Claudia Valenzuela, Athol U. Wells Eur Respir Monogr 2019; 86: 14-26 |   |
Quantitative CT analysis in ILD and the use of artificial intelligence on imaging of ILD Lucio Calandriello, Tahreema Matin, Helmut Prosch, Joseph Jacob Eur Respir Monogr 2019; 86: 27-43 |   |
Pulmonary involvement in rheumatoid arthritis John A. Mackintosh, Anna Stainer, Laurens J. De Sadeleer, Carmel Stock, Wim A. Wuyts, Elisabetta A. Renzoni Eur Respir Monogr 2019; 86: 44-67 |   |
Pulmonary involvement in inflammatory myopathies Vincent Cottin, Thomas Barba, Sabine Mainbourg, Mouhamad Nasser, Claudia Valenzuela, Jean-Christophe Lega Eur Respir Monogr 2019; 86: 68-89 |   |
Pulmonary involvement in systemic sclerosis Athol U. Wells Eur Respir Monogr 2019; 86: 90-105 |   |
Pulmonary involvement in systemic lupus erythematosus, Sjögren syndrome and mixed connective tissue disease Katerina M. Antoniou, Eirini Vasarmidi, Athina Trachalaki, Eleni Bibaki, Bruno Crestani Eur Respir Monogr 2019; 86: 106-123 |   |
Pulmonary involvement in antiphospholipid syndrome Shaney L. Barratt, John D. Pauling, Nazia Chaudhuri Eur Respir Monogr 2019; 86: 124-139 |   |
Interstitial pneumonia with autoimmune features Alison M. DeDent, Aryeh Fischer Eur Respir Monogr 2019; 86: 140-152 |   |
Microscopic polyangiitis and granulomatosis with polyangiitis Christian Pagnoux Eur Respir Monogr 2019; 86: 153-172 |   |
Diffuse alveolar haemorrhage Martina Bonifazi, Stefan Stanel, George A. Margaritopoulos Eur Respir Monogr 2019; 86: 173-187 |   |
Eosinophilic granulomatosis with polyangiitis Vincent Cottin, Kais Ahmad, Mouhamad Nasser, Claudia Valenzuela, Matthieu Groh, Benjamin Terrier, Julie Traclet Eur Respir Monogr 2019; 86: 188-209 |   |
Pulmonary involvement in Takayasu arteritis and Behçet disease Veronica Alfieri, George A. Margaritopoulos Eur Respir Monogr 2019; 86: 210-227 |   |
Airway and lung involvement in inflammatory bowel disease Philippe Camus, Thomas V. Colby Eur Respir Monogr 2019; 86: 228-261 |   |
The lung in liver disease: hepatopulmonary syndrome and portopulmonary hypertension Sebastiano Emanuele Torrisi, Valentin Fuhrmann, Dirk Skowasch, Michael Kreuter Eur Respir Monogr 2019; 86: 262-277 |   |
Lung complications of neuromuscular diseases Elissavet Konstantelou, Eirini Pasparaki, Vasilios Tzilas, Eleni Bibaki, Yiorgos Meletis, Emmanouil Ferdoutsis, Argyris Tzouvelekis, Demosthenes Bouros Eur Respir Monogr 2019; 86: 278-295 |   |
Amyloidosis and the lung Jean-Simon Rech, Pierre-Yves Brillet, Florence Jeny, Marianne Kambouchner, Hilario Nunes, Bertrand Arnulf, Dominique Valeyre, Yurdagül Uzunhan Eur Respir Monogr 2019; 86: 296-318 |   |
Trafficking and lysosomal storage disorders Paolo Spagnolo, Jelle R. Miedema, Jan H. von der Thüsen, Marlies S. Wijsenbeek Eur Respir Monogr 2019; 86: 319-332 |   |
Pulmonary involvement in haematological disorders and bone marrow transplant recipients Venerino Poletti, Sara Colella, Sara Piciucchi, Marco Chilosi, Alessandra Dubini, Sissel Kronborg-White, Sara Tomassetti, Claudia Ravaglia Eur Respir Monogr 2019; 86: 333-358 |   |
Pulmonary involvement of systemic histiocytic disorders Davide Elia, Antonella Caminati, Roberto Cassandro, Sergio Harari Eur Respir Monogr 2019; 86: 359-373 |   |
Pulmonary involvement in immunodeficiency Elisabeth Bendstrup, Martina Vasakova Eur Respir Monogr 2019; 86: 374-390 |   |
Telomere syndrome and the lung Raphael Borie, Caroline Kannengiesser, Bruno Crestani Eur Respir Monogr 2019; 86: 391-403 |   |
Sarcoidosis: pulmonary manifestations and management Jonas Yserbyt, Athol U. Wells Eur Respir Monogr 2019; 86: 404-418 |   |