Monograph

The ERS Monograph is the quarterly book series from the ERS.

Each Monograph covers a specific area of respiratory medicine, providing in-depth reviews that give clinicians at all levels a concise, comprehensive guide to symptoms, diagnosis and treatment.

Idiopathic Pulmonary Fibrosis

European Respiratory Society Monograph, Vol. 71. 2016
ISBN (electronic): 978-1-84984-068-2
DOI: 10.1183/2312508X.erm7116

Idiopathic pulmonary fibrosis (IPF) is a steadily progressive and ultimately fatal disease of unknown origin. Recent years have seen advances in our understanding of IPF and a number of guidelines have been published. But many questions remain unanswered, particularly surrounding probable versus definite IPF. This Monograph aims to discuss the latest achievements in IPF, and covers key diagnostic issues, staging of the disease, complications and comorbidities, treatment, unmet patient needs and perspectives for the future. This book will be of interest to all clinicians and researchers in this area.

Preface Robert Bals Eur Respir Monogr 2016; 71: v-vi
Guest Editors Eur Respir Monogr 2016; 71: vii-ix
Introduction Ulrich Costabel, Bruno Crestani, Athol U. Wells Eur Respir Monogr 2016; 71: x-xi
List of abbreviations Eur Respir Monogr 2016; 71: xii
Epidemiology Vidya Navaratnam, Doug L. Forrester, Richard B. Hubbard Eur Respir Monogr 2016; 71: 1-15
Genetics Raphael Borie, Caroline Kannengiesser, Nadia Nathan, Bruno Crestani Eur Respir Monogr 2016; 71: 16-34
Pathogenesis Benjamin Loeh, Martina Korfei, Poornima Mahavadi, Roxana Wasnick, Daniel von der Beck, Andreas Günther Eur Respir Monogr 2016; 71: 35-49
Key diagnostic issues Dominique Valeyre, Florence Jeny, Olivia Freynet, Hilario Nunes Eur Respir Monogr 2016; 71: 50-56
Histopathology and cryobiopsy Venerino Poletti, Sara Tomassetti, Claudia Ravaglia, Alessandra Dubini, Sara Piciucchi, Alberto Cavazza, Marco Chilosi Eur Respir Monogr 2016; 71: 57-73
Bronchoalveolar lavage Tiago M. Alfaro, Carlos Robalo Cordeiro Eur Respir Monogr 2016; 71: 74-81
Imaging Simon L.F. Walsh Eur Respir Monogr 2016; 71: 82-96
The evaluation of disease severity/staging for prognosis Oisin J. O'Connell, Jim J. Egan Eur Respir Monogr 2016; 71: 97-105
Monitoring Katrin Milger, Jürgen Behr Eur Respir Monogr 2016; 71: 106-121
Biomarkers Maria A. Kokosi, Elisabetta Renzoni, Francesco Bonella Eur Respir Monogr 2016; 71: 122-142
Acute exacerbations Antje Prasse Eur Respir Monogr 2016; 71: 143-150
Cancer Carlo Vancheri Eur Respir Monogr 2016; 71: 151-159
Pulmonary hypertension Etienne-Marie Jutant, Laura Price, S. John Wort, Marc Humbert, David Montani Eur Respir Monogr 2016; 71: 160-174
CPFE: distinctive and non-distinctive features Athol U. Wells, George A. Margaritopoulos, Katerina M. Antoniou, Hilario Nunes, Ulrich Costabel Eur Respir Monogr 2016; 71: 175-185
Other comorbidities Michael Kreuter, Eva Brunnemer, Svenja Ehlers-Tenenbaum, Nicolas Kahn, Jacques Bruhwyler, Martin Kolb Eur Respir Monogr 2016; 71: 186-195
Pharmacological management Vincent Cottin, Claudia Valenzuela Eur Respir Monogr 2016; 71: 196-217
Symptom management: dyspnoea and cough Wim A. Wuyts Eur Respir Monogr 2016; 71: 218-229
Nonpharmacological interventions: rehabilitation, palliative care and transplantation Klaus Kenn, Rainer Gloeckl, Inga Heinzelmann, Nikolaus Kneidinger Eur Respir Monogr 2016; 71: 230-242
Key patients' needs: a patient's perspective Derek Ross Eur Respir Monogr 2016; 71: 243-252
Key ongoing issues in trial design Mark G. Jones, Luca Richeldi Eur Respir Monogr 2016; 71: 253-259
Perspectives for the future Toby M. Maher, Paolo Spagnolo Eur Respir Monogr 2016; 71: 260-274