Monograph

The ERS Monograph is the quarterly book series from the ERS.

Each Monograph covers a specific area of respiratory medicine, providing in-depth reviews that give clinicians at all levels a concise, comprehensive guide to symptoms, diagnosis and treatment.

Orphan Lung Diseases

European Respiratory Society Monograph, Vol. 54. 2011

ISBN: 978-1-84984-013-2

DOI: 10.1183/1025448x.erm5410

Rare lung diseases are one of the most exciting topics in respiratory medicine. However, as these are infrequent diseases evidence-based guidelines do not exist for most of the different entities. Nevertheless, progress has been made during the last decade either in diagnostics or therapy, which has greatly changed clinical practice. This issue of the European Respiratory Monograph, with contributions from well-known experts in the field, summarises the current knowledge of orphan lung disease in one edition for the first time. This allows respiratory physicians, either in the clinic or in research, to obtain an overview about the whole field of these diseases.

Guest Editor Eur Respir Monogr 2011; 54: v
Preface T. Welte Eur Respir Monogr 2011; 54: vi
Introduction J-F. Cordier Eur Respir Monogr 2011; 54: vii-viii
Granulomatosis with polyangiitis (Wegener&s) D. Nelson, U. Specks Eur Respir Monogr 2011; 54: 1-14
Alveolar haemorrhage syndromes R. Lazor Eur Respir Monogr 2011; 54: 15-31
Pulmonary involvement in Behçet&s disease and Takayasu&s arteritis O. Uzun Eur Respir Monogr 2011; 54: 32-45
Multiple cystic lung diseases J-F. Cordier, S.R. Johnson Eur Respir Monogr 2011; 54: 46-83
Bronchiolitis V. Poletti, G. Casoni, M. Zompatori, A. Carloni, A. Cancellieri, M. Chilosi Eur Respir Monogr 2011; 54: 84-103
Interstitial lung disease with autoimmune features B.W. Kinder Eur Respir Monogr 2011; 54: 104-117
Idiopathic eosinophilic pneumonias V. Cottin Eur Respir Monogr 2011; 54: 118-139
Churg–Strauss syndrome L. Guillevin, B. Dunogue, C. Pagnoux Eur Respir Monogr 2011; 54: 140-151
Amyloidosis and the lung J.H. Pinney, H.J. Lachmann Eur Respir Monogr 2011; 54: 152-170
Alveolar lipoproteinosis syndromes F. Bonella, D. Theegarten, J. Guzman, U. Costabel Eur Respir Monogr 2011; 54: 171-186
Idiopathic tracheopathies J.H. Ryu, F. Maldonado, S. Tomassetti Eur Respir Monogr 2011; 54: 187-200
Primary ciliary dyskinesia J.S.A. Lucas, W.T. Walker, C.E. Kuehni, R. Lazor Eur Respir Monogr 2011; 54: 201-217
Pulmonary arteriovenous malformations and other pulmonary aspects of HHT C.L. Shovlin, P. Wilmshurst, J.E. Jackson Eur Respir Monogr 2011; 54: 218-245
Hepatopulmonary syndrome: a liver-induced oxygenation defect G. Martínez-Palli, R. Rodríguez-Roisin Eur Respir Monogr 2011; 54: 246-264
Thoracic endometriosis and catamenial pneumothorax A. Bobbio, R. Trisolini, D. Damotte, M. Alifano Eur Respir Monogr 2011; 54: 265-281
Smoking-related interstitial lung disease S. Cerri, P. Spagnolo, F. Luppi, L. Richeldi Eur Respir Monogr 2011; 54: 282-300
Rare interstitial lung diseases of environmental origin C. Robalo Cordeiro, T.M. Alfaro, S. Freitas, J. Cemlyn-Jones, A.J. Ferreira Eur Respir Monogr 2011; 54: 301-316
Pulmonary hypertension in orphan lung diseases D. Montani, L. Bertoletti, X. Jais, P. Dorfmuller, L. Price, B. Girerd, O. Sitbon, M. Humbert, G. Simonneau Eur Respir Monogr 2011; 54: 317-331
Rare indications for lung transplantation J. Gottlieb Eur Respir Monogr 2011; 54: 332-340
Pseudo-tumours and reciprocal mimics of neoplastic and non-neoplastic pulmonary disorders N. Girard, J-F. Cordier Eur Respir Monogr 2011; 54: 341-365