Towards a better understanding of rare diffuse parenchymal lung diseases

Oral Presentation
Chairs: F. Bonella (Düsseldorf, Germany), C. McCarthy (Dublin 4, Ireland)
Tolerance and efficacy of antifibrotic treatments in IPF patients carriying telomere related gene mutations
A. Justet (Paris , France), D. Klay (Utrecht, Netherlands), V. Cottin (Lyon, France), M. Molina Molina (Barcelona, Spain), H. Nunes (Bobigny, France), M. Reynaud-Gaubert (Marseille, France), J. Naccache (Paris , France), E. Manali (Athens, Greece), A. Froidure (Bruxelles, France), S. Jouneau ( Rennes, Belgium), L. Wemeau (Lille, France), C. Andrejak (Amiens , France), A. Gondouin (Besançon, France), S. Hirschi (Strasbourg, France), B. Bondue (Bruxelles , Belgium), P. Bonniaud (Dijon , France), C. Tromeur (Brest, France), G. Prevost (Toulouse, France), S. Marchand-Adam (Tours, France), M. Funke-Chambour (Bern, Switzerland), A. Gamez (Montpellier, France), C. Kanengiesser (Paris, France), C. Van Moorsel (Utrecht, Netherlands), B. Crestani (Paris, France), R. Borie (Paris , France)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Clinical impact of BRAFV600E mutation in adult pulmonary Langerhans cell histiocytosis
A. Tazi (Paris, France), F. Jouenne (Paris, France), E. Bugnet (Paris, France), G. Lorillon (Paris, France), V. Meignin (Paris, France), A. Sadoux (Paris, France), S. Chevret (Paris, France), S. Mourah (Paris, France)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Effectiveness of various therapy regimens for patients with pulmonary Langerhans cell histiocytosis during long-term follow-up
A. Zinchenko (Saint-Petersburg, Russian Federation), L. Novikova (Saint-Petersburg, Russian Federation), M. Ilkovich (Saint-Petersburg, Russian Federation)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Natural history of incidental sporadic or tuberous sclerosis complex associated lymphangioleiomyomatosis
F. Di Marco (Milano, Italy), S. Terraneo (Milano, Italy), O. Olívia Meira Dias (Sao Paulo, Brazil), G. Imeri (Milan, Italy), S. Centanni (Milan, Italy), L. Giuliani (Milan, Italy), E. Lesma (Milan, Italy), G. Palumbo (Milan, Italy), M. Wanderley (Sao Paulo, Brazil), C. Ribeiro Carvalho (Sao Paulo, Brazil), B. Guedes Baldi (Sao Paulo, Brazil)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Early-onset therapy with sirolimus helps to improve prognosis of patients with lymphangioleiomyomatosis (LAM)
M. Klingenberg (Hannover, Germany), J. Freise (Hannover, Germany), J. Fuge (Hannover, Germany), T. Welte (Hannover, Germany)
Congress or journal article abstractWebcastSlide presentationE-poster
Congress or journal article abstractWebcastSlide presentationE-poster
Pulmonary Alveolar Microlithiasis ~ Epidemiology in Japan and Developing treatment strategies in a novel mouse model ~
A. Saito (Sapporo, Japan), R. Takamiya (Tokyo, Japan), N. Fujitani (Sapporo, Japan), S. Ariki (Sapporo, Japan), K. Kuronuma (Sapporo, Japan), H. Chiba (Sapporo, Japan), M. Takahashi (Sapporo, Japan), H. Takahashi (Sapporo, Japan)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation
Disease patterns in connective tissue disease-associated interstitial lung disease: a population based study
C. Hyldgaard (Silkeborg, Denmark), E. Bendstrup (Aarhus, Denmark), A. Pedersen (Aarhus, Denmark), L. Pedersen (Aarhus, Denmark), T. Ellingsen (Odense, Denmark)
Congress or journal article abstractWebcastSlide presentation
Congress or journal article abstractWebcastSlide presentation