The changing face of rare diffuse parenchymal lung diseases: recent advances in pathogenesis, clinical manifestations and treatment

Thematic Poster
Chairs: M. Kokosi (London, United Kingdom), E. Radzikowska (Warszawa, Poland), R. Borie (Paris, France), C. Valenzuela (Madrid, Spain)
Role of the COX2- PGE2 axis in S. pneumoniae- induced pulmonary fibrosis exacerbation in mice.
T. Bormann (Hannover, Germany), R. Maus (Hannover, Germany), J. Stolper (Hannover, Germany), M. Moog (Hannover, Germany), L. Knudsen (Hannover, Germany), T. Welte (Hannover, Germany), M. Kolb (Hamilton, Canada), U. Maus (Hannover, Germany)
Congress or journal article abstract
Congress or journal article abstract
Transcriptomic profiling of CD4 lymphocytes in a murine model of AdTGFß-1 induced lung fibrosis
C. Hinze (Hannover, Germany), M. Moog (Hannover, Germany), R. Maus (Hannover, Germany), D. Deluca (Hannover, Germany), T. Welte (Hannover, Germany), M. Kolb (Ontario, Canada), U. Maus (Hannover, Germany)
Congress or journal article abstract
Congress or journal article abstract
BMS-986278, a lysophosphatidic acid 1 (LPA1) receptor antagonist, in healthy participants: A single/multiple ascending dose (SAD/MAD) phase 1 study
G. Tirucherai (Princeton, United States of America), D. Yu (Silverado, United States of America), R. Revankar (Princeton, United States of America), G. Klinger (Princeton, United States of America), J. Van Lier (Groningen, Netherlands), J. Taubel (London, United Kingdom), T. Correll (Princeton, United States of America)
Congress or journal article abstractE-poster
Congress or journal article abstractE-poster
BMS-986327 as a novel PET imaging agent for assessment of LPA1 receptors in IPF
R. Smith (Princeton, United States of America), J. Kim (Princeton, United States of America), D. Donnelly (Princeton, United States of America), A. Andrea Olga Shorts (Princeton, United States of America), T. Petrone (Princeton, United States of America), S. Kalinowski (Princeton, United States of America), B. Murphy (Princeton, United States of America), P. Cheng (Princeton, United States of America), T. Correll (Princeton, United States of America), P. Chow (Princeton, United States of America), S. Shuyan Du (Princeton, United States of America), S. Bonacorsi (Princeton, United States of America), W. Hayes (Princeton, United States of America)
Congress or journal article abstract
Congress or journal article abstract
A rare diagnosis: Hermansky-Pudlak syndrome in a patient with pulmonary fibrosis, oculocutaneous albinism and thrombocytopathy
M. Doubková (Brno, Czech Republic), J. Trizuljak (Brno, Czech Republic), A. Hrazdirová (Brno, Czech Republic), Z. Vrzalová (Brno, Czech Republic), I. Blaháková (Brno, Czech Republic), L. Radová (Brno, Czech Republic), Š. Pospíšilová (Brno, Czech Republic), M. Doubek (Brno, Czech Republic)
Congress or journal article abstract
Congress or journal article abstract
Effectiveness of corticosteroid in diffuse alveolar hemorrhage with hematologic malignancy
K. Song (Seoul, Republic of Korea), J. Ahn (Seoul, Republic of Korea), Y. Koh (Seoul, Republic of Korea)
Congress or journal article abstract
Congress or journal article abstract
Perception of the caregivers of patients with idiopathic pulmonary fibrosis: results of the French national survey, RESPIR
S. Marchand-Adam (Tours, France), A. Bourdin (Montpellier, France), E. Bergot (Caen, France), H. Nunes (Bobigny, France), B. Wallaert (Lille, France), G. Prévot (Toulouse, France), V. Cottin (Lyon, France)
Congress or journal article abstractE-poster
Congress or journal article abstractE-poster
Psychological predictors of health-related quality of life of interstitial lung disease patients.
C. Zepeda-Dominguez (Mexico , Mexico), V. Pelaez-Hernandez (Mexico , Mexico), C. Pineda-Sanchez (Mexico , Mexico), V. Pachicano-Romero (Mexico , Mexico), A. Orea-Tejeda (Mexico , Mexico), A. Ibarra-Fernandez (Mexico , Mexico), L. Luna-Rodriguez (Mexico , Mexico), A. Martinez-Bautista (Mexico , Mexico), D. Gonzalez-Islas (Mexico , Mexico), K. Rosales-Castillo (Mexico , Mexico), R. Sanchez-Santillan (Mexico , Mexico), A. Flores-Vargas (Mexico , Mexico), K. Balderas-Muñoz (Mexico , Mexico), R. Davila-Ramos (Mexico , Mexico), A. Jimenez-Valentin (Mexico , Mexico), F. Salgado-Fernandez (Mexico , Mexico), S. Hernandez-Lopez (Mexico , Mexico), Y. Pilozi-Montiel (Mexico , Mexico)
Congress or journal article abstract
Congress or journal article abstract
Psychological abnormalities are commonly present in adult patients with pulmonary Langerhans cell histiocytosis
A. Tazi (Paris, France), E. Bugnet (Paris, France), N. Gupta (Cincinnati, United States of America), G. Lorillon (Paris, France), S. Arbabzadeh-Bouchez (Paris, France), J. Lépine (Paris, France), S. Chevret (Paris, France)
Congress or journal article abstractE-poster
Congress or journal article abstractE-poster
Expectations of patients suffering from idiopathic pulmonary fibrosis about their treatment: results of the French national survey, RESPIR
A. Bourdin (Montpellier, France), E. Bergot (Caen, France), H. Nunes (Bobigny, France), G. Prévot (Toulouse, France), B. Wallaert (Lille, France), S. Marchand-Adam (Tours, France), V. Cottin (Lyon, France)
Congress or journal article abstractE-poster
Congress or journal article abstractE-poster
Segment by segment lavage as an excellent alternative treatment in pulmonary alveolar proteinosis in a 3 years old boy.
s. yousefzadegan (Tehran, Islamic Republic of Iran), M. Modaresi (Tehran, Islamic Republic of Iran), R. Shirzadi (Tehran, Islamic Republic of Iran), S. Navaie (Tehran, Islamic Republic of Iran), M. Ghaempanah (Tehran, Islamic Republic of Iran)
Congress or journal article abstractE-poster
Congress or journal article abstractE-poster
Cicatricial lung fibrosis: five cases
M. Samsonova (Moscow, Russian Federation), A. Cherniaev (Moscow, Russian Federation), K. Mikhailichenko (Moscow, Russian Federation)
Congress or journal article abstractE-poster
Congress or journal article abstractE-poster
Assessment of Treatment Response in Granulomatous Lymphocytic Interstitial Lung Disease (GLILD)
G. Gkrepi (Andros, Greece), D. Lowe (London, United Kingdom), S. Burns (London, United Kingdom), S. Seneviratne (London, United Kingdom), J. Hurst (London, United Kingdom)
Congress or journal article abstractE-poster
Congress or journal article abstractE-poster
Interstitial lung disease in CVID (GLILD): clinical presentation and comparison to CVID without ILD
V. Somogyi (Heidelberg, Germany), M. Eichinger (Heidelberg, Germany), F. Lasitschka (Heidelberg, Germany), J. Kappes (Heidelberg, Germany), M. Kreuter (Heidelberg, Germany)
Congress or journal article abstractE-poster
Congress or journal article abstractE-poster
Macrolides as a potential treatment in organizing pneumonia
A. Fonseca Carriço (Guarda, Portugal), P. Caetano (Porto, Portugal), N. Melo (Porto, Portugal), H. Novais Bastos (Porto, Portugal), S. Guimarães (Porto, Portugal), C. Souto Moura (Porto, Portugal), J. Pereira (Porto, Portugal), A. Morais (Porto, Portugal)
Congress or journal article abstract
Congress or journal article abstract
Analysis of hospitalizations by lymphangioleiomyomatosis in Spain
J. Teran Tinedo (Madrid, Spain), F. Pedraza Serrano (Madrid, Spain), C. Castro Riera (Madrid, Spain), Z. Ji (Madrid, Spain), A. López De Andrés (Madrid, Spain), R. Jiménez García (Madrid, Spain), V. Hernández Barrera (Madrid, Spain), L. Puente Maestu (Madrid, Spain), J. De Miguel Diez (Madrid, Spain)
Congress or journal article abstract
Congress or journal article abstract
CLINICO-PATHOLOGICAL PATTERNS OF THE THORACIC ENDOMETRIOSIS.
I. Dvorakovskaya (St. Petersburg, Russian Federation), B. Ariel (St. Petersburg, Russian Federation), L. Novikova (St. Petersburg, Russian Federation), P. Yablonskiy (St. Petersburg, Russian Federation)
Congress or journal article abstractE-poster
Congress or journal article abstractE-poster
Gender perspective in Interstitial Lung Diseases (ILD)
E. De Freitas Gonzalez (León, Spain), J. Juan García (León, Spain), R. Almeida Cabrera (León, Spain), C. Mier Bango (León, Spain), C. López Garay (León, Spain), E. Bollo De Miguel (León, Spain), I. Herráez Ortega (León, Spain), N. Alonso Orcajo (León, Spain), L. Sierra Herranz (León, Spain)
Congress or journal article abstract
Congress or journal article abstract