Pulmonary Manifestations of Systemic Diseases

European Respiratory Society Monograph, Vol. 86. 2019
ISBN (electronic): 978-1-84984-112-2
DOI: 10.1183/2312508X.erm8619

Interest in interstitial lung diseases (ILDs) has risen in recent years. A large volume of basic and clinical research has increased our understanding of the pathogenesis of idiopathic pulmonary fibrosis (IPF) and non-IPF fibrotic ILDs. The ILD field is now evolving rapidly, with major implications for practical management. This Monograph provides expert clinical guidance on these difficult diseases, which will be helpful to both respiratory and nonrespiratory physicians alike. The initial chapters consider diagnostic issues, pulmonary function tests and techniques that are currently in development. The book then goes on to cover a variety of pulmonary manifestations of very different disease entities, such as connective tissue diseases, systemic vasculitis and much more.


Preface
John R. Hurst
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Guest Editors

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Introduction
Wim A. Wuyts, Vincent Cottin, Paolo Spagnolo, Athol U. Wells
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List of abbreviations

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Multidisciplinary approach to systemic diseases: benefits for diagnosis and management of complex disorders
Fabrizio Luppi, Paola Faverio, Wim A. Wuyts
Eur Respir Monogr 2019; 86: 1-13
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Pulmonary function tests in multisystem disorders: prejudices and pitfalls
Claudia Valenzuela, Athol U. Wells
Eur Respir Monogr 2019; 86: 14-26
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Quantitative CT analysis in ILD and the use of artificial intelligence on imaging of ILD
Lucio Calandriello, Tahreema Matin, Helmut Prosch, Joseph Jacob
Eur Respir Monogr 2019; 86: 27-43
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Pulmonary involvement in rheumatoid arthritis
John A. Mackintosh, Anna Stainer, Laurens J. De Sadeleer, Carmel Stock, Wim A. Wuyts, Elisabetta A. Renzoni
Eur Respir Monogr 2019; 86: 44-67
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Pulmonary involvement in inflammatory myopathies
Vincent Cottin, Thomas Barba, Sabine Mainbourg, Mouhamad Nasser, Claudia Valenzuela, Jean-Christophe Lega
Eur Respir Monogr 2019; 86: 68-89
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Pulmonary involvement in systemic sclerosis
Athol U. Wells
Eur Respir Monogr 2019; 86: 90-105
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Pulmonary involvement in systemic lupus erythematosus, Sjögren syndrome and mixed connective tissue disease
Katerina M. Antoniou, Eirini Vasarmidi, Athina Trachalaki, Eleni Bibaki, Bruno Crestani
Eur Respir Monogr 2019; 86: 106-123
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Pulmonary involvement in antiphospholipid syndrome
Shaney L. Barratt, John D. Pauling, Nazia Chaudhuri
Eur Respir Monogr 2019; 86: 124-139
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Interstitial pneumonia with autoimmune features
Alison M. DeDent, Aryeh Fischer
Eur Respir Monogr 2019; 86: 140-152
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Microscopic polyangiitis and granulomatosis with polyangiitis
Christian Pagnoux
Eur Respir Monogr 2019; 86: 153-172
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Diffuse alveolar haemorrhage
Martina Bonifazi, Stefan Stanel, George A. Margaritopoulos
Eur Respir Monogr 2019; 86: 173-187
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Eosinophilic granulomatosis with polyangiitis
Vincent Cottin, Kais Ahmad, Mouhamad Nasser, Claudia Valenzuela, Matthieu Groh, Benjamin Terrier, Julie Traclet
Eur Respir Monogr 2019; 86: 188-209
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Pulmonary involvement in Takayasu arteritis and Behçet disease
Veronica Alfieri, George A. Margaritopoulos
Eur Respir Monogr 2019; 86: 210-227
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Airway and lung involvement in inflammatory bowel disease
Philippe Camus, Thomas V. Colby
Eur Respir Monogr 2019; 86: 228-261
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The lung in liver disease: hepatopulmonary syndrome and portopulmonary hypertension
Sebastiano Emanuele Torrisi, Valentin Fuhrmann, Dirk Skowasch, Michael Kreuter
Eur Respir Monogr 2019; 86: 262-277
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Lung complications of neuromuscular diseases
Elissavet Konstantelou, Eirini Pasparaki, Vasilios Tzilas, Eleni Bibaki, Yiorgos Meletis, Emmanouil Ferdoutsis, Argyris Tzouvelekis, Demosthenes Bouros
Eur Respir Monogr 2019; 86: 278-295
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Amyloidosis and the lung
Jean-Simon Rech, Pierre-Yves Brillet, Florence Jeny, Marianne Kambouchner, Hilario Nunes, Bertrand Arnulf, Dominique Valeyre, Yurdagül Uzunhan
Eur Respir Monogr 2019; 86: 296-318
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Trafficking and lysosomal storage disorders
Paolo Spagnolo, Jelle R. Miedema, Jan H. von der Thüsen, Marlies S. Wijsenbeek
Eur Respir Monogr 2019; 86: 319-332
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Pulmonary involvement in haematological disorders and bone marrow transplant recipients
Venerino Poletti, Sara Colella, Sara Piciucchi, Marco Chilosi, Alessandra Dubini, Sissel Kronborg-White, Sara Tomassetti, Claudia Ravaglia
Eur Respir Monogr 2019; 86: 333-358
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Pulmonary involvement of systemic histiocytic disorders
Davide Elia, Antonella Caminati, Roberto Cassandro, Sergio Harari
Eur Respir Monogr 2019; 86: 359-373
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Pulmonary involvement in immunodeficiency
Elisabeth Bendstrup, Martina Vasakova
Eur Respir Monogr 2019; 86: 374-390
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Telomere syndrome and the lung
Raphael Borie, Caroline Kannengiesser, Bruno Crestani
Eur Respir Monogr 2019; 86: 391-403
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Sarcoidosis: pulmonary manifestations and management
Jonas Yserbyt, Athol U. Wells
Eur Respir Monogr 2019; 86: 404-418
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