Lung fibrosis in Pulmonary Alveolar Proteinosis (PAP): different stages of a syndrome or distinct diseases?

F. Mariani (Pavia (PV), Italy), C. Infusino (Pavia (PV), Italy), S. Lettieri (Pavia (PV), Italy), D. Piloni (Pavia (PV), Italy), M. Bosio (Pavia (PV), Italy), A. De Silvestri (Pavia (PV), Italy), A. Corino (Pavia (PV), Italy), I. Campo (Pavia (PV), Italy)

Source: Virtual Congress 2021 – Clinical evolution, management and outcomes of patients with rare diffuse parenchymal lung diseases

Congress or journal article abstractE-poster

Rating: 0
You must login to grade this presentation.

Share or cite this content

Citations should be made in the following way:
F. Mariani (Pavia (PV), Italy), C. Infusino (Pavia (PV), Italy), S. Lettieri (Pavia (PV), Italy), D. Piloni (Pavia (PV), Italy), M. Bosio (Pavia (PV), Italy), A. De Silvestri (Pavia (PV), Italy), A. Corino (Pavia (PV), Italy), I. Campo (Pavia (PV), Italy). Lung fibrosis in Pulmonary Alveolar Proteinosis (PAP): different stages of a syndrome or distinct diseases?. 2369

You must login to share this Presentation/Article on Twitter, Facebook, LinkedIn or by email.

Member's Comments

No comment yet.
You must Login to comment this presentation.


Related content which might interest you:
Diffuse dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: A distinct entity or a variant of idiopathic pulmonary fibrosis?
Source: International Congress 2014 – ILDs 1
Year: 2014


Familial pulmonary fibrosis: Respiratory function progression analysis in different HRCT patterns
Source: International Congress 2015 – IPF: clinical aspects II
Year: 2015


Assessment of telomere length in the combined pulmonary fibrosis and emphysema syndrome
Source: International Congress 2014 – ILDs: diagnostic and prognostic investigations
Year: 2014


Comparison of physiological impairment in ILD patients with and without diagnostic IPF features
Source: International Congress 2014 – ILDs 4
Year: 2014


Early effect of whole lung lavage (WLL) on surfactant homeostasis in pulmonary alveolar proteinosis (PAP)
Source: International Congress 2014 – ILDs: diagnostic and prognostic investigations
Year: 2014



Proportion of idiopathic pulmonary fibrosis among interstitial lung disease in a tertiary care center and its response to treatment
Source: International Congress 2014 – ILDs 5
Year: 2014


Clinical features of four children with pulmonary alveolar proteinosis
Source: International Congress 2014 – ILDs 5
Year: 2014


Pulmonary hypertension in different interstitial lung diseases
Source: Annual Congress 2012 - Diffuse parenchymal lung disease: clinical profiles and collagen vascular disease
Year: 2012


Loss of PTEN induced lung fibroblasts exhibiting similar pathogenic features to cancer cells in idiopathic pulmonary fibrosis
Source: International Congress 2014 – ILDs 2
Year: 2014


Relation between pulmonary arterial remodeling and parenchymal disease in severe COPD and interstitial lung disease patients
Source: International Congress 2014 – Pulmonary hypertension in lung disease
Year: 2014

Evolution of an interstitial lung disease MDT: 5.5 years of data
Source: International Congress 2014 – ILDs: pathogenesis and clinical features
Year: 2014


Changes in the small airways in idiopathic pulmonary fibrosis
Source: Annual Congress 2013 –Idiopathic pulmonary fibrosis and rarities
Year: 2013

Club cell secretory protein-CC16 is increased in idiopathic pulmonary fibrosis
Source: International Congress 2016 – ILD pathogenesis
Year: 2016


The decline in lung function is related to both emphysema and fibrosis extent in patients with idiopathic pulmonary fibrosis (IPF)/ combined pulmonary fibrosis and emphysema (CPFE)
Source: International Congress 2014 – ILDs 1
Year: 2014


Epithelial mesenchymal transition in fibroblastic foci of different fibrosing lung diseases: Repair or remodeling?
Source: Annual Congress 2013 –Idiopathic pulmonary fibrosis: pathogenesis
Year: 2013

Variation in mortality from interstitial lung disease by diagnosis
Source: International Congress 2015 – IIPs: orphan
Year: 2015


6MWT performance by means of Spiropalm in patients affected by fibrotic idiopathic interstitial pneumonias: Preliminary observations
Source: International Congress 2014 – ILDs 6
Year: 2014


Airway centered interstitial fibrosis – An under-recognized type of idiopathic interstitial pneumonia
Source: International Congress 2014 – ILDs: pathogenesis and clinical features
Year: 2014


Idiopathic pulmonary fibrosis is associated with a preferential alteration of kCO rather than of DLCO
Source: International Congress 2014 – ILDs 6
Year: 2014


Difference in the dynamic state between SP-A and SP-D in the IPF lung
Source: Annual Congress 2013 –Diffuse pulmonary fibrosis
Year: 2013