The role of noninvasive ventilation in the management of type II respiratory failure in patients with myotonic dystrophy

Vilma Rautemaa, Mark E. Roberts, Andrew Bentley, Timothy W. Felton

Source: ERJ Open Res, 7 (3) 00192-2020; 10.1183/23120541.00192-2020
Journal Issue: July
Disease area: Respiratory critical care, Sleep and breathing disorders

Congress or journal article abstractFull text journal articlePDF journal article, handout or slides

Rating: 0
You must login to grade this presentation.

Share or cite this content

Citations should be made in the following way:
Vilma Rautemaa, Mark E. Roberts, Andrew Bentley, Timothy W. Felton. The role of noninvasive ventilation in the management of type II respiratory failure in patients with myotonic dystrophy. ERJ Open Res, 7 (3) 00192-2020; 10.1183/23120541.00192-2020

You must login to share this Presentation/Article on Twitter, Facebook, LinkedIn or by email.

Member's Comments

No comment yet.
You must Login to comment this presentation.


Related content which might interest you:
Inspiratory muscle dysfunction relates to clinical disease severity in patients with type I myotonic dystrophy
Source: International Congress 2019 – Lung function and respiratory muscle testing
Year: 2019

Factors influencing compliance to long-term respiratory therapies in patients with myotonic dystrophy type 1
Source: International Congress 2017 – Noninvasive ventilation for chronic respiratory failure
Year: 2017

Unplanned respiratory crises requiring ventilation in Duchenne muscular dystrophy (DMD) patients can be reduced by timely respiratory review and care co-ordination at the age of transition
Source: Annual Congress 2012 - Current trends in home mechanical ventilation
Year: 2012


Evolution of patients with myotonic dystrophy and home mechanical ventilation
Source: Eur Respir J 2007; 30: Suppl. 51, 316s
Year: 2007

Pulmonary function in Duchenne muscular dystrophy patients before and after noninvasive ventilation
Source: Eur Respir J 2005; 26: Suppl. 49, 85s
Year: 2005

Mouthpiece ventilation in Duchenne muscular dystrophy
Source: International Congress 2016 – New horizons for noninvasive ventilation in acute and chronic settings
Year: 2016


Effect on survival of long-term non-invasive ventilation and cardiac management for Duchenne muscular dystrophy
Source: Eur Respir J 2006; 28: Suppl. 50, 184s
Year: 2006

Role of noninvasive ventilation in the child with syndromic disorder or neuromuscular disease presenting with acute respiratory failure
Source: Sleep and Breathing Conference 2017
Year: 2017

Myotonic dystrophy: feasibility and modalities of non-invasive ventilation to treat SDB
Source: Sleep and Breathing Conference 2017
Year: 2017

Chronic respiratory failure in myotonic dystrophy type 1 (DM1): Incidence & risk factors
Source: International Congress 2017 – Clinical and physiological challenges in noninvasive ventilation
Year: 2017

Hypercapnic ventilatory response in patients with Steinert's myotonic dystrophy type 1
Source: Annual Congress 2013 –Clinical respiratory physiology in different diseases
Year: 2013

Evolution and survival of patients with Myotonic Distrophy and non-invasive ventilation.
Source: International Congress 2017 – Noninvasive ventilation for chronic respiratory failure
Year: 2017


Introduction of domiciliary mechanical insufflation-exsufflation can reduce the incidence of crisis admissions in patients with Duchenne muscular dystrophy (DMD)
Source: Annual Congress 2012 - Current trends in home mechanical ventilation
Year: 2012


Age of loss of walking ability in patients with Duchenne muscular dystrophy: A marker for the elective use of mechanical ventilation?
Source: Annual Congress 2011 - Exercise tests and emerging outcomes: defining the impact of pulmonary rehabilitation
Year: 2011

Nocturnal efficacy of servo-adaptative ventilation in patient with Type 1 myotonic dystrophy (MD1)
Source: Annual Congress 2010 - Long-term noninvasive ventilation in the chronic patient: outcome and pathophysiology
Year: 2010

Influence of bulbar paralyis and noninvasive ventilation on survival in ALS patients with chronic respiratory failure
Source: Eur Respir J 2007; 30: Suppl. 51, 317s
Year: 2007

Effects of respiratory muscle training on strength and heart rate variability in myotonic dystrophy patients
Source: Annual Congress 2010 - Respiratory muscles and breathing: assessment and training
Year: 2010

Risk factors for the need mechanical ventilatory support in patients with duchenne muscular dystrophy
Source: Annual Congress 2010 - Respiratory muscle function and training in acute and chronic respiratory disease
Year: 2010

Home-based versus hospital monitoring of respiratory function changes in Duchenne muscular dystrophy (DMD)
Source: International Congress 2018 – Management of chronic cough and respiratory muscle dysfunction
Year: 2018

Nocturnal efficacy of two modalities of non-invasive mechanical ventilation (NIMV) in patients with Steinert‘s dystrophy
Source: Eur Respir J 2007; 30: Suppl. 51, 242s
Year: 2007