Analysis of the MILES cohort reveals determinants of disease progression and treatment response in lymphangioleiomyomatosis

Nishant Gupta, Hye-Seung Lee, Lisa R. Young, Charlie Strange, Joel Moss, Lianne G. Singer, Koh Nakata, Alan F. Barker, Jeffrey T. Chapman, Mark L. Brantly, James M. Stocks, Kevin K. Brown, Joseph P. Lynch, Hilary J. Goldberg, Gregory P. Downey, Angelo M. Taveira-DaSilva, Jeffrey P. Krischer, Kenneth Setchell, Bruce C. Trapnell, Yoshikazu Inoue, Francis X. McCormack

Source: Eur Respir J, 53 (4) 1802066; 10.1183/13993003.02066-2018
Journal Issue: April

Congress or journal article abstractFull text journal articlePDF journal article, handout or slides

Rating: 0
You must login to grade this presentation.

Share or cite this content

Citations should be made in the following way:
Nishant Gupta, Hye-Seung Lee, Lisa R. Young, Charlie Strange, Joel Moss, Lianne G. Singer, Koh Nakata, Alan F. Barker, Jeffrey T. Chapman, Mark L. Brantly, James M. Stocks, Kevin K. Brown, Joseph P. Lynch, Hilary J. Goldberg, Gregory P. Downey, Angelo M. Taveira-DaSilva, Jeffrey P. Krischer, Kenneth Setchell, Bruce C. Trapnell, Yoshikazu Inoue, Francis X. McCormack. Analysis of the MILES cohort reveals determinants of disease progression and treatment response in lymphangioleiomyomatosis. Eur Respir J, 53 (4) 1802066; 10.1183/13993003.02066-2018

You must login to share this Presentation/Article on Twitter, Facebook, LinkedIn or by email.

Member's Comments

No comment yet.
You must Login to comment this presentation.


Related content which might interest you:
Risk factors for lung disease progression in children with cystic fibrosis; a longitudinal cohort study
Source: International Congress 2017 – Cystic fibrosis: treatments and monitoring
Year: 2017

Identification and analysis of clinical phenotypes in COPD patients: PALOMB Cohort
Source: Virtual Congress 2021 – COPD burden, epidemiology and management
Year: 2021


Disease progression at 12 months does not predict future outcomes in IPF patients: Analysis from the Australian IPF Registry
Source: International Congress 2017 – ILDs: clinical aspects
Year: 2017

Blood biomarkers predicting disease progression in patients with IPF: data from the INMARK trial
Source: International Congress 2019 – The evolving field of idiopathic interstitial pneumonia
Year: 2019




CF-ABLE-UK score: Modification and validation of a clinical prediction rule for prognosis in cystic fibrosis on data from UK CF registry
Source: International Congress 2015 – Cystic fibrosis: physiology, biomarkers, microbiology and miscellaneous
Year: 2015


Risk factors for active tuberculosis in patients with inflammatory bowel disease: A case-control study
Source: International Congress 2015 – Latent TB infection and screening
Year: 2015


Identification of clinical phenotypes in patients with and without COPD using cluster analysis
Source: International Congress 2016 – Biomarkers and phenotypes of COPD and comorbidities
Year: 2016


Predicting mortality in idiopathic pulmonary fibrosis. Which parameters should be used to determine eligibility for treatment? Analysis of a UK prospective cohort
Source: International Congress 2016 – The best is yet to come in terms of lung function
Year: 2016



Presence of concurrent sarcoid-like granulomas indicates better survival in cancer patients: a retrospective cohort study
Source: ERJ Open Res, 6 (4) 00061-2020; 10.1183/23120541.00061-2020
Year: 2020



Does timeliness of diagnosis influence survival and treatment response in idiopathic pulmonary fibrosis?  Real- world results from the EMPIRE registry.
Source: International Congress 2017 – Idiopathic pulmonary fibrosis: from the bench to the bedside
Year: 2017

PROOF-registry: A prospective observational registry to describe the disease course and outcomes of IPF patients in a real-world clinical setting- An interim report
Source: International Congress 2015 – IPF: clinical aspects
Year: 2015


Survival estimates in European cystic fibrosis patients and the impact of socioeconomic factors: a retrospective registry cohort study
Source: Eur Respir J, 58 (3) 2002288; 10.1183/13993003.02288-2020
Year: 2021



PROOF-registry: A prospective observational registry to describe the disease course and outcomes of idiopathic pulmonary fibrosis patients in a real-world clinical setting
Source: International Congress 2014 – ILDs 6
Year: 2014


Rheumatoid arthritis-related interstitial lung disease (RA-ILD): Clinical, functional features, and variables associated poor initial prognosis in a chilean cohort
Source: Virtual Congress 2020 – Clinical aspects and new treatment strategies for rare interstitial lung diseases in adults and children
Year: 2020

Does anti-acid treatment influence disease progression in SSc-ILD ? data from the German SSc-network
Source: International Congress 2019 – Connective tissue disease-associated interstitial lung disease and hypersensitivity pneumonitis: what’s new?
Year: 2019



Efficacy of rituximab in patients with connective tissue disease associated interstitial lung disease: Preliminary results in safety and clinical response
Source: Annual Congress 2012 - Diffuse parenchymal lung disease pathogenesis, biomarkers, therapy and new entities
Year: 2012


Monitoring disease progression in patients with biopsy proven cases of sarcoidosis: A survey
Source: Annual Congress 2010 - Sarcoidosis: from the bench to the bedside
Year: 2010

MUC2MUC5B and TOLLIP variants: no association with disease progression and survival in an IPF cohort
Source: Virtual Congress 2020 – Biomarkers and mechanistic aspects of idiopathic pulmonary fibrosis
Year: 2020


Late Breaking Abstract - A composite serum biomarker index for the diagnosis of systemic sclerosis associated interstitial lung disease: a multicentre, observational, cohort study
Source: Virtual Congress 2021 – New approaches to diagnostic and prognostic evaluation of interstitial lung diseases of known causes
Year: 2021



Prognostic factors affecting survival of idiopathic pulmonary fibrosis in Korean population
Source: Eur Respir J 2007; 30: Suppl. 51, 578s
Year: 2007