Lung function, weight, and sweat chloride responses in patients with cystic fibrosis and the G551D-CFTR mutation treated with ivacaftor: A secondary analysis

S. Elborn, B. Plant, M. Konstan, R. Aherns, S. Rodriguez, A. Munck, C. Johnson (Belfast, United Kingdom; Cork, Ireland; Cleveland, Iowa City, Cambridge, United States Of America; Paris, France)

Source: Annual Congress 2013 –Cystic fibrosis: lung function and change of lung function in infants and children before and after treatment
Disease area: Paediatric lung diseases

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S. Elborn, B. Plant, M. Konstan, R. Aherns, S. Rodriguez, A. Munck, C. Johnson (Belfast, United Kingdom; Cork, Ireland; Cleveland, Iowa City, Cambridge, United States Of America; Paris, France). Lung function, weight, and sweat chloride responses in patients with cystic fibrosis and the G551D-CFTR mutation treated with ivacaftor: A secondary analysis. Eur Respir J 2013; 42: Suppl. 57, 5059

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